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纤维脂肪血管异常:一种罕见且常被误诊的病症。

Fibro Adipose Vascular Anomaly: A Rare and Often Misdiagnosed Entity.

作者信息

Khera Pushpinder S, Garg Pawan K, Babu Santhosh, Elhence Poonam, Tiwari Sarbesh, Nk Shyamkumar

机构信息

Department of Diagnostic and Interventional Radiology, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India.

Department of Pathology, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India.

出版信息

Indian J Radiol Imaging. 2021 Nov 13;31(3):776-781. doi: 10.1055/s-0041-1736399. eCollection 2021 Jul.

DOI:10.1055/s-0041-1736399
PMID:34790337
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8590565/
Abstract

Fibro adipose vascular anomaly (FAVA) is a rare type of vascular malformation with distinct clinical features. The authors here discussed the clinical, imaging, differential diagnosis, histopathological features, and treatment options of FAVA along with an illustrative case. It is important to know about this uncommon entity as this can be misdiagnosed due to the overlapping clinical features with other common entities. It is a benign condition with no proven malignant potential. There are no guidelines regarding the best treatment option.

摘要

纤维脂肪血管异常(FAVA)是一种具有独特临床特征的罕见血管畸形类型。本文作者讨论了FAVA的临床、影像学、鉴别诊断、组织病理学特征及治疗选择,并伴有一个说明性病例。了解这种不常见的疾病很重要,因为它可能因与其他常见疾病临床特征重叠而被误诊。它是一种良性疾病,尚无恶变潜能的确切证据。目前尚无关于最佳治疗方案的指南。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ff/8590565/2730f2129a88/10-1055-s-0041-1736399-i49720-4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ff/8590565/010298dd0782/10-1055-s-0041-1736399-i49720-1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ff/8590565/dc0322256ee5/10-1055-s-0041-1736399-i49720-2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ff/8590565/fd1c90601f28/10-1055-s-0041-1736399-i49720-3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ff/8590565/2730f2129a88/10-1055-s-0041-1736399-i49720-4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ff/8590565/010298dd0782/10-1055-s-0041-1736399-i49720-1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ff/8590565/dc0322256ee5/10-1055-s-0041-1736399-i49720-2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ff/8590565/fd1c90601f28/10-1055-s-0041-1736399-i49720-3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ff/8590565/2730f2129a88/10-1055-s-0041-1736399-i49720-4.jpg

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本文引用的文献

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2
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Pediatr Radiol. 2020 Mar;50(3):380-387. doi: 10.1007/s00247-019-04571-6. Epub 2019 Dec 13.
3
Fibroadipose Vascular Anomaly in the Upper Extremity: A Distinct Entity With Characteristic Clinical, Radiological, and Histopathological Findings.
下肢纤维脂肪血管异常
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4
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Medicine (Baltimore). 2024 Feb 16;103(7):e37225. doi: 10.1097/MD.0000000000037225.
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Pediatric Vascular Anomalies: A Clinical and Radiological Perspective.小儿血管异常:临床与放射学视角
Indian J Radiol Imaging. 2023 Sep 16;34(1):103-127. doi: 10.1055/s-0043-1774391. eCollection 2024 Jan.
6
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