Ranucci Giulia, Di Dato Fabiola, Liccardo Daniela, Spada Marco, Maggiore Giuseppe, Iorio Raffaele
Section of Pediatrics, Department of Translational Medical Science, University of Naples Federico II, Naples, Italy.
Hepatology, Gastroenterology, Nutrition and Liver Transplant Unit, IRCCS Bambino Gesù Pediatric Hospital, Rome, Italy.
Front Pediatr. 2021 Nov 1;9:766187. doi: 10.3389/fped.2021.766187. eCollection 2021.
Hepatic hydrothorax (HH) represents a rare complication of portal hypertension among adult cirrhotic patients. Here, we describe a pediatric case of HH, observed in a biliary atresia infant. The child presented with recurrent right-sided pleural effusion, after a successful Kasai portoenterostomy with restoration of bile flow and without overt signs of hepatic failure. Recurrence of HH led the patient to liver transplant despite a low pediatric end-stage liver disease value. Although rare, HH can also occur in children and should be suspected in patients with portal hypertension and respiratory distress. HH may be an indication for liver transplantation.
肝性胸水（HH）是成年肝硬化患者门静脉高压的一种罕见并发症。在此，我们描述了一例在胆道闭锁婴儿中观察到的小儿HH病例。该患儿在成功进行Kasai肝门空肠吻合术恢复胆汁流动且无明显肝衰竭迹象后，出现反复右侧胸腔积液。尽管小儿终末期肝病评分较低，但HH的复发仍导致该患者接受肝移植。尽管罕见，但HH也可发生于儿童，对于有门静脉高压和呼吸窘迫的患者应怀疑此病。HH可能是肝移植的一个指征。
