Division of Neurosurgery, Connecticut Children's, 282 Washington Street, Hartford, CT 06106, USA; Department of Surgery, UConn School of Medicine, 200 Academic Way, Farmington, CT 06032, USA.
Department of Surgery, UConn School of Medicine, 200 Academic Way, Farmington, CT 06032, USA; Divisions of Plastic Surgery and Craniofacial Surgery, Connecticut Children's, 282 Washington Street, Hartford, CT 06106, USA.
Neurosurg Clin N Am. 2022 Jan;33(1):105-112. doi: 10.1016/j.nec.2021.09.008. Epub 2021 Oct 26.
Craniosynostosis involves the premature fusion of 1 or more cranial sutures and commonly presents as an isolated, nonsyndromic diagnosis. A subset of patients have syndromic craniosynostosis. Several unique considerations must be taken into account when managing patients with syndromic craniosynostosis. A multidisciplinary craniofacial team with a central coordinator is particularly useful for coordinating care among various specialists, and close monitoring is mandatory owing to the increased risk of intracranial hypertension. Surgical management varies among centers, but core options include fronto-orbital advancement with cranial vault remodeling, posterior vault expansion, endoscopic-assisted suturectomy with postoperative orthotic therapy, and midface advancement.
颅缝早闭涉及 1 条或多条颅骨缝的过早融合，通常表现为孤立的、非综合征性诊断。一部分患者存在综合征性颅缝早闭。在管理综合征性颅缝早闭患者时，必须考虑一些独特的注意事项。多学科颅面团队和中央协调员特别有助于协调各个专家之间的护理，并且由于颅内压升高的风险增加，必须进行密切监测。手术管理因中心而异，但核心选择包括额眶前移和颅盖重塑、后颅扩张、内镜辅助缝切除术加术后矫形治疗以及中面部前移。
