Padilla Lichtenberger Fernando, Glerean Mariela, Paissan Andrea, Ajler Pablo
Servicio de Neurocirugía, Hospital Italiano de Buenos Aires, Argentina. E-mail:
Servicio de Endocrinología, Hospital Italiano de Buenos Aires, Argentina.
Medicina (B Aires). 2021;81(6):1069-1072.
Rathke's cleft cyst (RCC) are a slow-growing, benign, cystic lesions that arises from the remnants of the primitive ectoderm and Rathke's pouch. They present a common origin with pituitary adenomas (PA), however, the concomitant presentation of a PA and a RCC rarely occur. We present a case of a 41-year-old female with Cushing's disease. Magnetic resonance imaging (MRI) showed two synchronic lesions in the sellar region. An endoscopic transnasal approach was performed, with complete excision of both. The histological studies revealed an ACTH secreting PA and a RCC. The patient presented clinical and endocrinological remission six months after surgery. With the presence of cystic lesion at the sellar region, and the concomitant finding of a pituitary adenoma, RCC should be considered.
拉克氏囊肿（RCC）是一种生长缓慢的良性囊性病变，起源于原始外胚层和拉克氏囊的残余物。它们与垂体腺瘤（PA）有共同的起源，然而，PA和RCC同时出现的情况很少见。我们报告一例41岁患有库欣病的女性病例。磁共振成像（MRI）显示蝶鞍区有两个同步病变。采用经鼻内镜入路，将两者完全切除。组织学研究显示为分泌促肾上腺皮质激素的PA和RCC。患者术后6个月出现临床和内分泌缓解。当蝶鞍区出现囊性病变并同时发现垂体腺瘤时，应考虑RCC。
