From the Department of Anesthesiology, Walter Reed National Military Medical Center, Bethesda, Maryland.
Department of Anesthesiology, Stony Brook University, Stony Brook, New York.
A A Pract. 2021 Dec 10;15(12):e01541. doi: 10.1213/XAA.0000000000001541.
Native American Myopathy (NAM) is an inherited, malignant hyperthermia-susceptible myopathy associated with abnormal craniofacial development and neuromuscular scoliosis. There is scant NAM anesthetic literature and, to our knowledge, no existing publications describing the anesthetic management of a NAM parturient. The constellation of symptoms of NAM in the parturient presents a number of challenges to the obstetric anesthesiologist, including difficult airway associated with craniofacial abnormalities and pregnancy, malignant hyperthermia susceptibility, and possible difficult neuraxial block. In this report, we present the anesthetic management of a parturient with NAM and previous extensive posterior spinal fusion undergoing cesarean delivery under general anesthesia.
原发性先天性肌病（NAM）是一种遗传性、恶性高热易感肌病，与颅面发育异常和神经肌肉脊柱侧凸有关。关于 NAM 的麻醉文献很少，据我们所知，目前尚无关于 NAM 产妇的麻醉管理的出版物。NAM 产妇的症状组合给产科麻醉师带来了许多挑战，包括与颅面异常和妊娠相关的困难气道、恶性高热易感性以及可能的困难脊柱神经阻滞。在本报告中，我们介绍了一例 NAM 产妇和以前广泛后路脊柱融合术的麻醉管理，该产妇在全身麻醉下接受剖宫产。
