Björnsson S, Jóhannsson J H, Sigurjónsson F
Acta Med Scand. 1987;221(1):115-9. doi: 10.1111/j.0954-6820.1987.tb01252.x.
We report a patient with localized, primary gastric amyloidosis, who presented with recurrent hematemesis, a rare presentation for an unusual disease. The patient was initially thought to have stomach cancer because of the X-ray and gastroscopic appearance of the gastric mucosa, but was eventually found to have primary amyloidosis confined to the stomach and regional lymph nodes. The amyloid was found to be of immunoglobulin origin, AL amyloid. Other reports of localized gastric amyloidosis are reviewed and compared with the present case. Most of the patients were clinically suspected of gastric carcinoma, and only one had hematemesis. We propose that amyloidosis should be considered in the differential diagnosis of hematemesis and gastric tumors.
我们报告一例局限性原发性胃淀粉样变患者，该患者表现为反复呕血，这是一种罕见疾病的少见表现。由于胃黏膜的X线及胃镜表现，该患者最初被认为患有胃癌，但最终发现其原发性淀粉样变局限于胃及区域淋巴结。发现该淀粉样物质为免疫球蛋白源性，即AL淀粉样变。本文回顾了其他局限性胃淀粉样变的报道并与本病例进行比较。大多数患者临床上疑似胃癌，仅有一例出现呕血。我们建议在呕血和胃肿瘤的鉴别诊断中应考虑淀粉样变。
