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一名年轻男性患者的腹主动脉瘤破裂,罕见病例报告。

Ruptured abdominal aortic aneurysm in a young male patient, a rare case report.

作者信息

Lohani Kush Raj, Xin Geraldine Wong Yan, Cui Jiaqian, Sannasi Vikram Vijayan

机构信息

Division of Vascular Surgery, Department of General Surgery, Ng Teng Fong General Hospital, National University Health System, Singapore.

Division of Vascular Surgery, Department of General Surgery, Ng Teng Fong General Hospital, National University Health System, Singapore.

出版信息

Int J Surg Case Rep. 2022 Jan;90:106713. doi: 10.1016/j.ijscr.2021.106713. Epub 2021 Dec 22.

Abstract

INTRODUCTION AND IMPORTANCE

Abdominal aortic aneurysm (AAA) is commonly a disease of the elderly population with an atherosclerotic aorta. We present a rare case scenario of a large ruptured AAA in a young patient.

CASE PRESENTATION

A 32-year-old man presented to the Emergency Department with abdominal pain. On examination he had hypotension with a severely tender abdomen. Imaging revealed a ruptured 10 cm abdominal aortic aneurysm (AAA). He underwent an emergency open aneurysm repair and was discharged well on post-operative day 12. Apart from smoking, he had no known significant risk factors contributing to an AAA of such size. Clinical features and family history suggested a possible underlying connective tissue disorder.

CLINICAL DISCUSSION

A painful abdomen and hypotension in a young patient should prompt investigations to rule out a rare but life-threatening diagnosis of a ruptured AAA.

CONCLUSION

A possible underlying connective tissue disorder should be investigated for in any young patient presenting with an AAA.

摘要

引言与重要性

腹主动脉瘤(AAA)通常是一种发生于老年人群、伴有动脉粥样硬化主动脉的疾病。我们报告一例年轻患者发生大型破裂性腹主动脉瘤的罕见病例。

病例介绍

一名32岁男性因腹痛就诊于急诊科。检查发现他有低血压,腹部压痛明显。影像学检查显示一个10厘米的腹主动脉瘤破裂。他接受了急诊开放性动脉瘤修复手术,并于术后第12天康复出院。除吸烟外,他没有已知的导致如此大小腹主动脉瘤的重大危险因素。临床特征和家族史提示可能存在潜在的结缔组织疾病。

临床讨论

年轻患者出现腹痛和低血压应促使进行检查,以排除罕见但危及生命的破裂性腹主动脉瘤诊断。

结论

对于任何出现腹主动脉瘤的年轻患者,都应调查是否存在潜在的结缔组织疾病。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b095/8718574/ab01b525302a/gr1.jpg

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