Federal University of Rio Grande Do Sul, Porto Alegre, Rio Grande do Sul, Brazil.
Santa Casa Hospital Complex, Porto Alegre, Rio Grande do Sul, Brazil.
Childs Nerv Syst. 2022 Aug;38(8):1625-1629. doi: 10.1007/s00381-021-05441-z. Epub 2022 Jan 10.
Pineal anlage tumors (PAT) are extremely rare malignant tumors in the pediatric population considered to be a variant of pineoblastomas. These tumors are characterized by a combination of neuroectodermal and heterologous ectomesenchymal components. PAT can be clinically aggressive and has a propensity to cerebrospinal fluid (CSF) dissemination. So far, only 13 cases of these tumors have been reported in the literature.
In this article, we report the case of an anlage tumor in a 3-year-old girl with a rapidly aggressive course.
松果体芽细胞瘤(PAT)是一种极为罕见的儿童恶性肿瘤,被认为是成神经管细胞瘤的一种变体。这些肿瘤的特点是神经外胚层和异源中胚层成分的组合。PAT 可能具有侵袭性临床特征,并具有向脑脊液(CSF)扩散的倾向。到目前为止,文献中仅报道了 13 例此类肿瘤。
在本文中,我们报告了一例 3 岁女孩的芽细胞瘤病例,其病程迅速进展。