Maternal and Child Health Hospital of Hubei Province, Wuhan, China.
Department of School of Medicine, Wuhan University of science and technology, Wuhan, China.
J Obstet Gynaecol Res. 2022 Mar;48(3):869-874. doi: 10.1111/jog.15148. Epub 2022 Jan 10.
Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) is a rare congenital malformation of the female reproductive organs, including uterine dysplasia, blind hemivagina, and ipsilateral renal dysplasia. It has a serious impact on patients' quality of life and fertility. We report a rare case of OHVIRA with a complete septate uterus, ectopic dysplasia of the left kidney, left ectopic ureter, and three oblique vaginal septa. The dysplastic left kidney and the ectopic ureter were removed during laparoscopy. In addition, the two layers of vaginal septa, which were ignored in the past 10 years, were removed by hysteroscopy. As the detection rate of OHVIRA has gradually increased, manifestations that previous classification systems could not recapitulate have emerged. By retrieving the relevant cases, we have tried to propose a new classification system, which would allow clinicians to have a complete understanding of the manifestations of OHVIRA and would be helpful in the treatment of patients.
单侧隐阴道和同侧肾发育不全（OHVIRA）是一种罕见的女性生殖器官先天性畸形，包括子宫发育不良、盲侧阴道和同侧肾发育不良。它严重影响患者的生活质量和生育能力。我们报告了一例罕见的 OHVIRA 病例，该病例伴有完全纵隔子宫、左侧肾脏异位发育、左侧异位输尿管和三个斜阴道隔。在腹腔镜下切除了发育不良的左侧肾脏和异位输尿管。此外，10 年来被忽视的两层阴道隔通过宫腔镜切除。随着 OHVIRA 的检出率逐渐增高，出现了以往分类系统无法概括的表现。通过检索相关病例，我们尝试提出了一种新的分类系统，该系统可以使临床医生全面了解 OHVIRA 的表现，并有助于患者的治疗。
