Kahloun Rim, Ben Yahia Salim, Braham Dorra, Chebel Saber
Department of Ophthalmology, Les Ophtalmologistes Associés de Monastir, Monastir, Tunisia.
Internal Medicine, Private Practice, Monastir, Tunisia.
Neuroophthalmology. 2021 May 3;46(1):50-53. doi: 10.1080/01658107.2021.1887286. eCollection 2022.
We report a case of a 28-year-old otherwise healthy female patient who presented with blurred vision in her right eye related to multiple branch retinal artery occlusions confirmed by fluorescein angiography. Investigation revealed positive antinuclear antibodies and an interatrial septal aneurysm on transthoracic echocardiography. The patient was treated with oral prednisolone and aspirin. Two months after her initial presentation, she developed hearing loss and tinnitus. Ophthalmological examination revealed temporal inferior and nasal inferior branch retinal artery occlusions in the left eye. Magnetic resonance imaging of the brain showed multifocal T2 hyperintense lesions in cortical and subcortical areas as well as the corpus callosum consistent with Susac's syndrome. The diagnosis of Susac's syndrome should be kept in mind in young patients presenting with multiple or recurrent retinal artery occlusions even in the absence of associated systemic symptoms to not delay appropriate management.
我们报告了一例28岁的健康女性患者，她因右眼视力模糊就诊，荧光素血管造影证实为多发性视网膜分支动脉阻塞。检查发现抗核抗体阳性，经胸超声心动图显示房间隔瘤。患者接受口服泼尼松龙和阿司匹林治疗。首次就诊两个月后，她出现听力丧失和耳鸣。眼科检查发现左眼颞下和鼻下视网膜分支动脉阻塞。脑部磁共振成像显示皮质和皮质下区域以及胼胝体有多灶性T2高信号病变，符合Susac综合征。对于出现多发性或复发性视网膜动脉阻塞的年轻患者，即使没有相关的全身症状，也应考虑Susac综合征的诊断，以免延误适当的治疗。
