Department of Obstetrics and Gynecology, Wayne State University, Detroit, USA.
BMC Pregnancy Childbirth. 2022 Feb 1;22(1):90. doi: 10.1186/s12884-022-04427-2.
Women with pre-existing forms of familial cardiomyopathy are at increased risk for morbidity and mortality due to hemodynamic changes of pregnancy. There is a lack of consensus about the management and care for these patients given the rarity of this condition. This case represents possibly the youngest pregnant familial dilated cardiomyopathy patient to deliver and the youngest patient to be fitted for a wearable cardiac defibrillator in the postpartum period.
A 14-year-old gravida 1 with familial dilated cardiomyopathy presented late for prenatal care at 38 weeks, which precluded typical care plans including baseline and serial echocardiograms, medication management, and routine prenatal care. An echocardiogram showed severely decreased left ventricular systolic function compared to studies from one year prior. Three days later the patient presented in labor and had a spontaneous vaginal delivery complicated by postpartum hemorrhage. Her postpartum course was notable for persistence of decreased cardiac function testing and placement of a wearable cardiac defibrillator for prevention against life threatening arrhythmias.
This case report adds to the literature on pregnancy complicated by familial dilated cardiomyopathy and describes management best practices and considerations during the antepartum, intrapartum, and postpartum periods.
患有家族性心肌病的女性由于妊娠期间的血流动力学变化,其发病率和死亡率增加。由于这种情况罕见,因此对于这些患者的管理和护理尚无共识。该病例可能是分娩时年龄最小的患有家族性扩张型心肌病的孕妇,也是产后佩戴可穿戴心脏除颤器的年龄最小的患者。
一名 14 岁的初产妇,患有家族性扩张型心肌病,在妊娠 38 周时才进行晚期产前检查,这使典型的护理计划无法实施,包括基线和连续超声心动图、药物管理和常规产前检查。超声心动图显示与一年前的研究相比,左心室收缩功能严重下降。三天后,患者出现临产症状,并伴有产后出血的自发性阴道分娩并发症。她的产后过程中,心功能检测持续下降,为预防危及生命的心律失常,需要放置可穿戴心脏除颤器。
本病例报告增加了家族性扩张型心肌病合并妊娠的文献,描述了产前、产时和产后的最佳管理实践和注意事项。