Department of Dermatology, Acıbadem Mehmet Ali Aydınlar University School of Medicine, İstanbul, Turkey.
Cutis. 2021 Dec;108(6):E23-E25. doi: 10.12788/cutis.0425.
Secretan syndrome (SS) is a recurrent or chronic form of factitious lymphedema that usually affects the dorsal aspect of the hand and is accepted as a subtype of Munchausen syndrome. Secretan syndrome usually is induced by compression of the extremity by tourniquets, ligatures, cords, or similar equipment. This unconsciously motivated and consciously produced lymphedema is an expression of underlying psychiatric disease. Herein, we present a fluctuating case of SS involving the hand, with periods of severe lymphedema and those of complete amelioration, parallel to stressful and peaceful periods in the patient's personal life. We briefly review the current literature on SS to increase awareness among dermatologists, and we present information on the clinical portrait, diagnosis, and appropriate management of this peculiar and underreported disorder.
塞克雷坦综合征(SS)是一种复发性或慢性人为淋巴水肿,通常影响手部的背面,被认为是慕尼琛综合征的一种亚型。SS 通常是由止血带、结扎带、绳索或类似设备对四肢的压迫引起的。这种无意识的动机和有意识的产生的淋巴水肿是潜在精神疾病的表现。在此,我们介绍了一个手部波动的 SS 病例,伴有严重的淋巴水肿期和完全缓解期,与患者个人生活中的紧张和平静时期平行。我们简要回顾了 SS 的当前文献,以提高皮肤科医生的认识,并提供有关这种特殊且报道较少的疾病的临床特征、诊断和适当治疗的信息。