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肾病型胱氨酸病的长期眼部表现

Long-term ocular manifestations in nephropathic cystinosis.

作者信息

Kaiser-Kupfer M I, Caruso R C, Minkler D S, Gahl W A

出版信息

Arch Ophthalmol. 1986 May;104(5):706-11. doi: 10.1001/archopht.1986.01050170096030.

DOI:10.1001/archopht.1986.01050170096030
PMID:3518682
Abstract

Eight nephropathic-cystinotic patients having undergone renal transplantation seven to 14 years previously were studied. Serious ocular complications were noted in four of the eight cases not previously reported. These included posterior synechiae, deposition of crystals on the anterior lens surface, and decreased visual acuity accompanied by impaired visual function, as measured by psychophysical and electrodiagnostic tests when possible.

摘要

对8例7至14年前接受肾移植的肾性胱氨酸病患者进行了研究。在8例患者中有4例出现了严重的眼部并发症,此前未见报道。这些并发症包括虹膜后粘连、晶状体前表面晶体沉积,以及视敏度下降并伴有视功能受损,视功能受损在可能的情况下通过心理物理学和电诊断测试来衡量。

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