Goraya Gurparvesh S, Singhal Sachi, Paul Birinder S, Paul Gunchan
Neurology, Dayanand Medical College and Hospital, Ludhiana, IND.
Internal Medicine, Crozer-Chester Medical Center, Upland, USA.
Cureus. 2022 Jan 24;14(1):e21568. doi: 10.7759/cureus.21568. eCollection 2022 Jan.
Vertebral hemangiomas (VHs) are benign vascular tumors that develop from the endoderm of blood vessels, although their exact pathogenesis is poorly understood. Most hemangiomas are small, about a third are multiple in number, and a very small number of these hemangiomas cause symptoms. Even more rare are aggressive VHs, which comprise a small number of all VHs, and are associated with expansion and extraosseous extension into the paraspinal and epidural spaces. Management of aggressive VHs involve pre-op embolization, spinal surgery, and reconstruction. Pain management, physical rehabilitation, and close neurological follow-up are imperative to near-total recovery. Aggressive VHs are most commonly seen in the thoracic region but may rarely involve a large number of vertebrae. Cutaneous hemangiomas, when seen along with VHs, are often metameric. We present a rare and challenging case of compressive myelopathy and a large cutaneous hemangioma or a "purple shoulder", found during an exam in a young male. He was found to have an extensive VH extending through 13 vertebral levels (C7 to D12), non-metameric to the cutaneous lesion. A thorough physical examination and evaluation along with prompt surgical treatment were the cornerstone of treatment and prevention of permanent neurological deficits.
椎体血管瘤(VHs)是起源于血管内胚层的良性血管肿瘤,但其确切发病机制尚不清楚。大多数血管瘤较小,约三分之一为多发,且这些血管瘤中只有极少数会引起症状。侵袭性VHs更为罕见,在所有VHs中占少数,与向椎旁和硬膜外间隙的扩展及骨外延伸有关。侵袭性VHs的治疗包括术前栓塞、脊柱手术和重建。疼痛管理、身体康复以及密切的神经学随访对于近乎完全康复至关重要。侵袭性VHs最常见于胸部区域,但很少累及多个椎体。当皮肤血管瘤与VHs同时出现时,通常是节段性的。我们报告了一例罕见且具有挑战性的病例,一名年轻男性在检查中发现患有压迫性脊髓病和一个巨大的皮肤血管瘤,即“紫色肩部”。他被发现有一个广泛的VH,延伸至13个椎体节段(C7至D12),与皮肤病变无节段对应关系。全面的体格检查和评估以及及时的手术治疗是治疗和预防永久性神经功能缺损的基石。