“缺失”的单侧肺动脉并非真正缺失，而是未连接。基于 4 例病例的当前文献复习。
"Absent" unilateral pulmonary arteries aren't absent, but disconnected. Review of the current literature based on 4 cases.
机构信息
Department of Pediatric Cardiology, Erasmus Medical Center, Sophia Children's Hospital, 3015CN Rotterdam, Netherlands.
Department of Cardiothoracic Surgery, Erasmus Medical Center, 3015GD Rotterdam, Netherlands.
出版信息
Rev Cardiovasc Med. 2022 Jan 25;23(2):46. doi: 10.31083/j.rcm2302046.
BACKGROUND
Disconnected unilateral pulmonary arteries are frequently misdiagnosed as "absent". They typically arise from the base of the innominate artery and are fed by an aberrant arterial duct. If diagnosed early enough, they can be reconnected with catheter techniques even after closure of this aberrant duct. Consecutive surgical anatomical correction at a later stage is possible.
METHODS
Four cases illustrate the anatomical findings on computed tomography and angiography, all show an outpouching at the base of the brachiocephalic artery.
RESULTS
The therapeutic approach consisted of stenting of the aberrant ductus and consecutive surgery. In the oldest patient, 13 years, such an approach was impossible.
CONCLUSION
If identified early in life, disconnected pulmonary arteries can be recruited with catheter techniques, and reconnected surgically at a later stage. It is not yet known if this approach prevents pulmonary damage, which is frequently seen in older untreated patients.
背景
孤立性肺动脉不连接通常被误诊为“缺失”。它们通常起源于无名动脉根部，并由异常的动脉导管供血。如果诊断足够早，即使在这个异常导管关闭后，也可以通过导管技术重新连接。随后在后期阶段进行连续的手术解剖矫正也是可能的。
方法
4 个病例说明了计算机断层扫描和血管造影的解剖发现，均显示在头臂动脉根部有一个膨出。
结果
治疗方法包括对异常导管进行支架置入和随后的手术。在最年长的患者（13 岁）中，这种方法是不可能的。
结论
如果在生命早期发现，孤立性肺动脉可以通过导管技术募集，并在后期进行手术重新连接。目前还不知道这种方法是否可以预防在未治疗的年长患者中经常见到的肺部损伤。
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