Hurtado Rodrigo, Guirales Fabian, Wang Alexandria, Hamid Bilal, Okabe Anna, Castro Eduardo, Tirado Carlos A
The International Circle of Genetics Studies.
William Paterson University (WPU), Wayne, NJ.
J Assoc Genet Technol. 2022;48(1):17-23.
Acute myeloid leukemia (AML) presents as a heterogeneous blood cancer characterized by the proliferation of immature myeloid cells. We present the case of an 18-year-old female with AML whose symptoms include marked leukocytosis, anemia, as well as thrombocytopenia with spontaneous cerebellar and intracerebral bleeds. The bone marrow biopsy is hypercellular and is expunged by sheets of blast cells with dispersed chromatin, prominent nucleoli, highly irregular nuclei, and moderate cytoplasm. Chromosome analysis reveals an abnormal karyotype with a derivative trisomy 8 and a derivative chromosome 16. The karyotype is described as 47,XX,+der(8)add(8)(q24.3),der(16) inv(16)(p13.1q22)del(16)(q22)[21]/46,XX[1]. DNA FISH analysis reveals abnormalities for RUNX1T1 (8q21.3) and CBFB (16q22) genes. These findings align with that of conventional cytogenetics. The National Comprehensive Cancer Network guidelines for AML state that CBFB gene rearrangements indicate that the patient falls under the favorable risk category. However, AML with core binding factor molecular aberrations is a heterogeneous group and thus the interaction with further cytogenetic abnormalities may result in further pathogenesis. Clinical correlation was suggested.
急性髓系白血病(AML)是一种异质性血液癌症,其特征为未成熟髓系细胞的增殖。我们报告了一例18岁女性AML患者,其症状包括明显的白细胞增多、贫血以及血小板减少,并伴有自发性小脑和脑内出血。骨髓活检显示细胞增多,有大量原始细胞片,染色质分散,核仁突出,核高度不规则,胞质中等。染色体分析显示核型异常,有衍生三体8和衍生染色体16。核型描述为47,XX,+der(8)add(8)(q24.3),der(16) inv(16)(p13.1q22)del(16)(q22)[21]/46,XX[1]。DNA荧光原位杂交(FISH)分析显示RUNX1T1(8q21.3)和CBFB(16q22)基因存在异常。这些发现与传统细胞遗传学结果一致。美国国立综合癌症网络(National Comprehensive Cancer Network)的AML指南指出,CBFB基因重排表明该患者属于低危类别。然而,伴有核心结合因子分子异常的AML是一个异质性群体,因此与进一步的细胞遗传学异常相互作用可能会导致进一步的发病机制。建议进行临床相关性研究。