Hachiro Kohei, Kinoshita Takeshi, Shiraishi Shoichiro, Suzuki Tomoaki
Department of Cardiovascular Surgery, Omi Medical Center, Kusatsu, Japan.
Kyobu Geka. 2022 Feb;75(2):88-91.
Situs inversus totalis is a congenital anomaly characterized by a mirror image transposition of the normal visceral organs, which makes it difficult to perform aortic surgery accurately. Stanford type A aortic dissection in patients with this condition is very rare and difficult to assess and manage. We report a case of Stanford type A aortic dissection with situs inversus totalis. The patient presented with severe tricuspid regurgitation with annulus enlargement due to chronic atrial fibrillation, requiring ascending aortic replacement and tricuspid annuloplasty. These procedures were performed after the operator swapped the left and right positions during the operation. Postoperative course was uneventful. By carefully checking the preoperative computed tomography images and changing the operator's position during the operation, it is possible to safely perform Stanford type A aortic dissection surgery in patients with situs inversus totalis.
完全性内脏反位是一种先天性异常,其特征是正常内脏器官呈镜像转位,这使得准确进行主动脉手术变得困难。患有这种情况的患者发生A型主动脉夹层非常罕见,且难以评估和处理。我们报告一例患有完全性内脏反位的A型主动脉夹层病例。该患者因慢性房颤出现严重三尖瓣反流伴瓣环扩大,需要进行升主动脉置换和三尖瓣环成形术。这些手术是在术者在手术过程中交换了左右位置后进行的。术后过程顺利。通过仔细检查术前计算机断层扫描图像并在手术过程中改变术者位置,可以安全地对完全性内脏反位患者进行A型主动脉夹层手术。