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胸壁巨大淋巴管瘤 1 例:新生儿罕见表现。

A Case Report of Huge Lymphangioma over the Chest Wall: A Rare Presentation of a Newborn.

机构信息

Department of Pediatrics and Child Health, Jimma University, Jimma, Ethiopia.

Department of Surgery, Jimma University, Jimma, Ethiopia.

出版信息

Ethiop J Health Sci. 2022 Jan;32(1):209-212. doi: 10.4314/ejhs.v32i1.22.

Abstract

BACKGROUND

Lymphangioma is a rare benign tumor of lymphatic system that is often diagnosed in the first few years of life. The presentation and complications depend on the site and the size of the lesion.

CLINICAL DESCRIPTION

This was a term male newborn weighing 3230g born to a 38 year old para IIV mother. Delivery was spontaneous and uneventful. The neonate was active, had no gross dysmorphic feature except the huge, 20cm by 28cm cystic, non-tender mass over the left lateral chest area.

DIAGNOSIS

Lymphangioma was diagnosed based on chest ultrasound, there was a large multiloculated cystic lesion over left lateral chest, and the cyst had no communication with spinal canal, and had no solid component.

THERAPY

The patient was observed for complications, otherwise not needing intervention in the first few days.

OUTCOMES

He developed superinfection of the mass, for which intravenous antibiotics administered, infection was controlled and surgery was postponed until a few months. However, the patient was presented with severe malnutrition at the age of three months and subsequently lost to follow up.

CONCLUSION

Huge lymphangiomas at neonatal age are likely to get superinfected; a close observation for signs of complications is needed. Though surgical intervention could be postponed until the baby grows to avoid the complications of surgery, adequate counseling is needed to reassure the parents about the benign and treatable nature of the disease. And individualized decision on earlier surgical intervention has to be considered with adequate postoperative care whenever follow up is not guaranteed.

摘要

背景

淋巴管瘤是一种罕见的淋巴系统良性肿瘤,通常在生命的头几年被诊断出来。其表现和并发症取决于病变的部位和大小。

临床描述

这是一名体重 3230 克的足月男婴,母亲为 38 岁初产妇 IV。分娩顺利,新生儿活跃,除了左侧侧胸有一个 20cm×28cm 的巨大囊性、无触痛的肿块外,无明显的大体畸形特征。

诊断

根据胸部超声诊断为淋巴管瘤,左侧侧胸有一个大的多房囊性病变,囊肿与椎管无相通,也没有实性成分。

治疗

患者在观察期间出现肿块继发感染,最初几天无需干预。

结果

他发生了肿块感染,给予了静脉抗生素,感染得到了控制,手术被推迟到几个月后。然而,患儿在三个月大时出现严重营养不良,随后失访。

结论

新生儿期的巨大淋巴管瘤容易继发感染,需要密切观察并发症的迹象。虽然可以等到婴儿长大后再进行手术干预以避免手术并发症,但需要向家长充分说明该疾病是良性和可治疗的,同时需要根据随访情况个体化决定是否早期进行手术干预,并提供充分的术后护理。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/83a0/8864385/1c8b63a4ace7/EJHS3201-0209Fig1.jpg

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本文引用的文献

1
Pathogenesis of lymphangiomas.淋巴管瘤的发病机制。
Virchows Arch. 2008 Jul;453(1):1-8. doi: 10.1007/s00428-008-0611-z. Epub 2008 May 24.
2
Cystic hygroma/lymphangioma: a rational approach to management.囊状水瘤/淋巴管瘤:一种合理的治疗方法。
Laryngoscope. 2001 Nov;111(11 Pt 1):1929-37. doi: 10.1097/00005537-200111000-00011.
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Cystic hygroma of the skull base.颅底囊肿性水瘤
Arch Otolaryngol Head Neck Surg. 1999 Dec;125(12):1390-3. doi: 10.1001/archotol.125.12.1390.
4
Cystic hygroma-lymphangioma: a rare and still unclear entity.囊状水瘤-淋巴管瘤:一种罕见且仍不清楚的病症。
Laryngoscope. 1989 Oct;99(10 Pt 2 Suppl 49):1-10. doi: 10.1288/00005537-198910001-00001.

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