Uman Navavee, Kobbuaklee Sirorat, Kansuwan Patsita, Watanaboonyongcharoen Phandee, Polprasert Chantana
Department of Medicine, Faculty of Medicine, Chulalongkorn University and King Chulalongkorn Memorial Hospital, Bangkok 10230, Thailand.
Research Unit in Translational Hematology, Chulalongkorn University, Bangkok 10230, Thailand.
Hematol Rep. 2022 Feb 28;14(1):13-18. doi: 10.3390/hematolrep14010003.
Background: Eosin-5-Maleimide (EMA)-based flow cytometry binds to red blood cell (RBC) membrane-associated proteins which can be used to detect red blood cell (RBC) membrane disorders. Myelodysplastic syndromes (MDS) are stem cell disorders resulting in ineffective hematopoiesis which is commonly present with anemia and erythroid dysplasia. Objectives: We aimed to study RBC membrane defects in MDS using flow cytometry for EMA staining. Methods: We enrolled anemic patients who were diagnosed with low-risk MDS (R-IPSS score ≤ 3.5), RBC membrane disorders [hereditary spherocytosis (HS) and Southeast Asian ovalocytosis (SAO)], and normal controls. Complete blood count (CBC) and flow cytometry for EMA staining were performed. Results: There were 16 cases of low-risk MDS, 6 cases of RBC membrane disorders, and 15 control cases. Mean fluorescence intensity (MFI) of EMA binding test in the RBC membrane disorders was significantly lower than controls (17.6 vs. 24.3, p < 0.001), but the EMA binding test in the low-risk MDS was not significantly different than the controls (26.5 vs. 24.3, p = 0.08). Conclusion: the RBC membrane defect in low-risk MDS was not demonstrated as having detection ability using EMA binding test with flow cytometry.
基于嗜酸性粒细胞-5-马来酰亚胺(EMA)的流式细胞术可结合红细胞(RBC)膜相关蛋白,用于检测红细胞膜疾病。骨髓增生异常综合征(MDS)是一种干细胞疾病,可导致无效造血,常伴有贫血和红系发育异常。目的:我们旨在通过EMA染色的流式细胞术研究MDS中的红细胞膜缺陷。方法:我们纳入了诊断为低危MDS(R-IPSS评分≤3.5)、红细胞膜疾病[遗传性球形红细胞增多症(HS)和东南亚椭圆形红细胞增多症(SAO)]的贫血患者以及正常对照。进行了全血细胞计数(CBC)和EMA染色的流式细胞术检测。结果:低危MDS患者16例,红细胞膜疾病患者6例,对照15例。红细胞膜疾病中EMA结合试验的平均荧光强度(MFI)显著低于对照组(17.6对24.3,p<0.001),但低危MDS中的EMA结合试验与对照组无显著差异(26.5对24.3,p=0.08)。结论:通过EMA结合试验和流式细胞术未显示低危MDS中的红细胞膜缺陷具有检测能力。