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额肌悬吊术治疗肌营养不良症:16年随访

Frontalis Suspension in Muscular Dystrophy: 16-years Follow-up.

作者信息

Abdulrauf Badr M I

机构信息

Section of Plastic Surgery, King Faisal Specialist Hospital and Research Center (General Organization), Jeddah, Saudi Arabia.

出版信息

Plast Reconstr Surg Glob Open. 2022 Mar 22;10(3):e4225. doi: 10.1097/GOX.0000000000004225. eCollection 2022 Mar.

Abstract

Acquired eyelid ptosis in adults, with complete loss of levator palpebrae superiosis function, can be a challenging problem to diagnose and treat. A 48-year-old woman with chronic bilateral severe blepharoptosis of 10 years duration is presented, whose neurological investigations excluded myasthenia gravis. The patient was preliminarily diagnosed with chronic progressive external ophthalmoplegia. The levator excursion was negligible, and a frontalis suspension procedure was considered using a conventional autogenous fascia lata graft. An optimal outcome was achieved with over 16-years follow-up. Although the patient was healthy otherwise upon first presentation, 10 years later, she developed other neurologic manifestations, including dysphagia and oral dryness. The fact that blepharoptosis did not recur over the years in this case differentiates an oculo-pharyngeal type of muscular dystrophy in this patient from other types and from the more frequent condition of chronic progressive external ophthalmoplegia.

摘要

成人获得性上睑下垂,提上睑肌功能完全丧失,诊断和治疗可能是一个具有挑战性的问题。本文介绍了一名48岁女性,患有持续10年的慢性双侧严重上睑下垂,其神经学检查排除了重症肌无力。该患者初步诊断为慢性进行性眼外肌麻痹。提上睑肌活动度可忽略不计,考虑使用传统的自体阔筋膜移植进行额肌悬吊手术。经过16年以上的随访,取得了最佳效果。尽管该患者初诊时其他方面健康,但10年后,她出现了其他神经学表现,包括吞咽困难和口腔干燥。该病例多年来上睑下垂未复发,这一事实将该患者的眼咽型肌营养不良与其他类型以及更常见的慢性进行性眼外肌麻痹区分开来。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/cb56/8939913/85fe73200bac/gox-10-e4225-g001.jpg

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