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Clinico-Pathological Features in Köhlmeier-Degos Disease with Cutaneous and Neurological Involvement.

作者信息

Sindhu Dodmallur Mallikarjuna, Shivaram Sumanth, Rao Shilpa, Nagappa Madhu, Seshagiri Doniparthi V, Santosh Vani, Madhukara J, Shreedhara A S, Bhat Maya D, Bharath Rose D, Sinha Sanjib

机构信息

Department of Neurology, National Institute of Mental Health and Neurosciences (NIMHANS), Bangalore, Karnataka, India.

Department of Neuropathology, National Institute of Mental Health and Neurosciences (NIMHANS), Bangalore, Karnataka, India.

出版信息

Ann Indian Acad Neurol. 2021 Nov-Dec;24(6):1005-1009. doi: 10.4103/aian.AIAN_1004_20. Epub 2021 Mar 27.

DOI:10.4103/aian.AIAN_1004_20
PMID:35359530
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8965922/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bbb1/8965922/0bebcacdf0c1/AIAN-24-1005-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bbb1/8965922/84a01f817e33/AIAN-24-1005-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bbb1/8965922/791bee446a7d/AIAN-24-1005-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bbb1/8965922/0bebcacdf0c1/AIAN-24-1005-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bbb1/8965922/84a01f817e33/AIAN-24-1005-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bbb1/8965922/791bee446a7d/AIAN-24-1005-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bbb1/8965922/0bebcacdf0c1/AIAN-24-1005-g003.jpg

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1
Clinico-Pathological Features in Köhlmeier-Degos Disease with Cutaneous and Neurological Involvement.伴有皮肤和神经受累的科尔迈尔-德戈斯病的临床病理特征。
Ann Indian Acad Neurol. 2021 Nov-Dec;24(6):1005-1009. doi: 10.4103/aian.AIAN_1004_20. Epub 2021 Mar 27.
2
Kohlmeier-Degos disease: a multisystem vasculopathy with progressive cerebral infarction.科尔迈尔-德戈斯病:一种伴有进行性脑梗死的多系统血管病。
Aust N Z J Med. 1991 Feb;21(1):49-51. doi: 10.1111/j.1445-5994.1991.tb03002.x.
3
[Case of disseminated intestinal and cutaneous thromboangiitis (Kohlmeier-Degos' syndrome)].[播散性肠道和皮肤血栓性血管炎(科尔迈尔-德戈斯综合征)病例]
Ter Arkh. 2010;82(2):54-6.
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The evolution of cerebrovascular changes in Köhlmeier-Degos disease: An 11-year follow-up case report.科尔迈尔-德戈斯病脑血管变化的演变:一例11年随访病例报告。
J Clin Neurosci. 2018 Feb;48:114-117. doi: 10.1016/j.jocn.2017.11.006. Epub 2017 Nov 26.
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[Malignant atrophic papulosis (Köhlmeier-Degos): diagnosis, therapy and course].[恶性萎缩性丘疹病(科尔迈尔-德戈斯病):诊断、治疗及病程]
Hautarzt. 2001 Aug;52(8):734-7. doi: 10.1007/s001050170092.
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An atypical paediatric case of malignant atrophic papulosis (Köhlmeier-Degos disease).一例非典型小儿恶性萎缩性丘疹病(科尔迈尔-德戈斯病)。
Eur J Pediatr. 1990 Apr;149(7):457-8. doi: 10.1007/BF01959394.
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Renovascular hypertension in a child with Degos-Köhlmeier disease.患有德戈斯-科尔迈尔病的儿童的肾血管性高血压。
Pediatr Radiol. 1987;17(3):260-1. doi: 10.1007/BF02388181.
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Enhanced cutaneous Rock2 expression as a marker of Rho Kinase pathway activation in autoimmune disease and Kohlemeier-Degos disease.增强的皮肤 Rock2 表达作为自身免疫性疾病和 Kohlemeier-Degos 病中 Rho 激酶途径激活的标志物。
Ann Diagn Pathol. 2020 Feb;44:151414. doi: 10.1016/j.anndiagpath.2019.151414. Epub 2019 Oct 23.
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[Benign course of malignant atrophic papulosis (Köhlmeier-Degos disease): lack of vessel occlusion as good prognostic sign?].[恶性萎缩性丘疹病(克勒迈尔-德戈斯病)的良性病程:血管未闭塞是良好的预后标志?]
J Dtsch Dermatol Ges. 2003 May;1(5):374-7. doi: 10.1046/j.1610-0387.2003.02015.x.
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Malignant and benign forms of atrophic papulosis (Köhlmeier-Degos disease): systemic involvement determines the prognosis.萎缩性丘疹病(Köhlmeier-Degos 病)的良恶性形式:全身性受累决定预后。
Br J Dermatol. 2014 Jan;170(1):110-5. doi: 10.1111/bjd.12642.

本文引用的文献

1
The evolution of cerebrovascular changes in Köhlmeier-Degos disease: An 11-year follow-up case report.科尔迈尔-德戈斯病脑血管变化的演变:一例11年随访病例报告。
J Clin Neurosci. 2018 Feb;48:114-117. doi: 10.1016/j.jocn.2017.11.006. Epub 2017 Nov 26.
2
A case of Degos disease in pregnancy.妊娠期德戈斯病1例。
Obstet Med. 2016 Dec;9(4):167-168. doi: 10.1177/1753495X16652006. Epub 2016 Jun 1.
3
Malignant atrophic papulosis (Köhlmeier-Degos disease) - a review.恶性萎缩性丘疹病(Köhlmeier-Degos 病)——综述。
Orphanet J Rare Dis. 2013 Jan 14;8:10. doi: 10.1186/1750-1172-8-10.
4
Infantile neurological Degos disease.婴儿神经型 Degos 病。
Eur J Paediatr Neurol. 2011 Mar;15(2):167-70. doi: 10.1016/j.ejpn.2010.06.003. Epub 2010 Jul 24.
5
Degos disease: a new simulator of non-accidental injury.德戈斯病:一种非意外损伤的新模拟病症。
Dev Med Child Neurol. 2009 Aug;51(8):647-50. doi: 10.1111/j.1469-8749.2009.03349.x. Epub 2009 Jun 22.
6
Case records of the Massachusetts General Hospital. Case 38-2006. A 5-year-old boy with headache and abdominal pain.马萨诸塞州总医院病例记录。病例38 - 2006。一名患有头痛和腹痛的5岁男孩。
N Engl J Med. 2006 Dec 14;355(24):2575-84. doi: 10.1056/NEJMcpc069029.
7
Optic nerve and spinal cord manifestations of malignant atrophic papulosis (Degos disease).恶性萎缩性丘疹病(德戈斯病)的视神经和脊髓表现
J Neurol Neurosurg Psychiatry. 2006 Feb;77(2):260-2. doi: 10.1136/jnnp.2005.066134.
8
Nervous system involvement in Degos disease.德戈斯病中的神经系统受累情况。
AJNR Am J Neuroradiol. 2005 Mar;26(3):646-9.
9
Skin lesion with a fatal neurologic outcome (Degos' disease).伴有致命神经学结局的皮肤病变(德戈斯病)
Neurology. 1996 Mar;46(3):636-40. doi: 10.1212/wnl.46.3.636.
10
CNS involvement in malignant atrophic papulosis (Kohlmeier-Degos disease): vasculopathy and coagulopathy.中枢神经系统受累于恶性萎缩性丘疹病(科尔迈尔-德戈斯病):血管病和凝血病。
J Neurol Neurosurg Psychiatry. 1981 Feb;44(2):156-60. doi: 10.1136/jnnp.44.2.156.