Azarfar Azin, Beg Shazia
Division of Rheumatology and Clinical Immunology, University of Florida, Gainesville, USA.
Rheumatology, University of Central Florida College of Medicine, Orlando, USA.
Cureus. 2022 Mar 3;14(3):e22824. doi: 10.7759/cureus.22824. eCollection 2022 Mar.
Achenbach syndrome, also known as "paroxysmal finger haematoma", is a rare, benign, self-limiting condition with unknown etiology that results in an acute onset swelling and pain, and subsequently blue discoloration of the fingers and sometimes the feet. The pathophysiology of this syndrome is not entirely clear, but intermittent spontaneous hematoma formation is reported as its characteristic symptom. Achenbach syndrome is more predominant in the female population. There are no known risk factors such as trauma, drug use, bleeding disorders, or rheumatologic diseases associated with the etiology of this syndrome. Although the symptoms are alarming to patients, the condition itself is not accompanied by any significant complications. Herein we present our case series of four patients experiencing symptoms compatible with the diagnosis of Achenbach syndrome. The aim of this study is to increase awareness of this condition and its benign nature to avoid unnecessary referrals or invasive procedures and investigations as well as alleviate the anxiety of patients.
阿亨巴赫综合征,也被称为“阵发性手指血肿”,是一种病因不明的罕见、良性、自限性疾病,其症状为手指急性肿胀、疼痛,随后手指(有时也包括足部)出现青肿。该综合征的病理生理学尚不完全清楚,但据报道间歇性自发血肿形成是其特征性症状。阿亨巴赫综合征在女性人群中更为常见。目前尚无已知的危险因素,如创伤、药物使用、出血性疾病或风湿性疾病与该综合征的病因相关。尽管这些症状会让患者感到担忧,但该疾病本身不会伴随任何严重并发症。在此,我们展示了4例有符合阿亨巴赫综合征诊断症状的患者病例系列。本研究的目的是提高对该疾病及其良性性质的认识,以避免不必要的转诊、侵入性检查和调查,同时减轻患者的焦虑。