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Linear Scleroderma of the Head - Updates in management of Parry Romberg Syndrome and En coup de sabre: A rapid scoping review across subspecialties.头部线性硬皮病——帕里-罗默伯格综合征和剑伤样硬皮病管理的最新进展：跨亚专业的快速范围综述
Eur J Rheumatol. 2020 Feb;7(Suppl1):S48-S57. doi: 10.5152/eurjrheum.2019.19183.
2
Tocilizumab in systemic sclerosis: a randomised, double-blind, placebo-controlled, phase 3 trial.托西珠单抗治疗系统性硬化症：一项随机、双盲、安慰剂对照、3 期临床试验。
Lancet Respir Med. 2020 Oct;8(10):963-974. doi: 10.1016/S2213-2600(20)30318-0. Epub 2020 Aug 28.
3
Is biological therapy in systemic sclerosis the answer?生物疗法是系统性硬化症的答案吗？
Rheumatol Int. 2020 May;40(5):679-694. doi: 10.1007/s00296-020-04515-6. Epub 2020 Jan 20.
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Linear scleroderma "en coup de sabre" with extensive brain involvement-Clinicopathologic correlations and response to anti-Interleukin-6 therapy.直线性硬皮病“砍状分布”伴广泛脑受累的临床病理相关性及抗白细胞介素-6 治疗的反应。
Orphanet J Rare Dis. 2019 May 16;14(1):110. doi: 10.1186/s13023-019-1015-7.
5
Consensus-based recommendations for the management of juvenile localised scleroderma.基于共识的青少年局限性硬皮病管理建议。
Ann Rheum Dis. 2019 Aug;78(8):1019-1024. doi: 10.1136/annrheumdis-2018-214697. Epub 2019 Mar 2.
6
Remission of seizures with immunosuppressive therapy in Parry-Romberg syndrome and en coup de sabre linear scleroderma: Case report and brief review of the literature.帕里-龙贝格综合征和剑伤样线状硬皮病采用免疫抑制疗法后癫痫发作缓解：病例报告及文献简要回顾
Pediatr Dermatol. 2018 Nov;35(6):e363-e365. doi: 10.1111/pde.13647. Epub 2018 Aug 31.
7
Magnetic Resonance Imaging Evaluation in Patients with Linear Morphea Treated with Methotrexate and High-Dose Corticosteroid.甲氨蝶呤和大剂量皮质类固醇治疗线状硬皮病患者的磁共振成像评估
Dermatol Res Pract. 2018 Jul 2;2018:8391218. doi: 10.1155/2018/8391218. eCollection 2018.
8
MRI for Dental Applications.牙科应用的磁共振成像
Dent Clin North Am. 2018 Jul;62(3):467-480. doi: 10.1016/j.cden.2018.03.006.
9
Development of minimum standards of care for juvenile localized scleroderma.制定青少年局限性硬皮病最低护理标准。
Eur J Pediatr. 2018 Jul;177(7):961-977. doi: 10.1007/s00431-018-3144-8. Epub 2018 May 4.
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Progressive Hemifacial Atrophy and Linear Scleroderma En Coup de Sabre: A Spectrum of the Same Disease?进行性半侧颜面萎缩和线性硬皮病剑伤样损害：是同一种疾病的不同表现吗？
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伴有剑击状硬皮病的帕里-龙贝格病：托珠单抗对牙周骨炎症的影响。

Parry Romberg disease with En Coup de Sabre Scleroderma: Effect of tocilizumab on periodontal bone inflammation.

作者信息

Meneghetti Thaís Cugler, da Silva Juliana Yassue Barbosa, Kluppel Lúcio Eduardo, de Carvalho Vânia Oliveira

机构信息

Unit of Pediatric Rheumatology, Waldemar Monastier Children's Hospital and Clinics Hospital, Federal University of Paraná, Curitiba, Brazil.

Positivo University, Curitiba, Brazil.

出版信息

J Scleroderma Relat Disord. 2021 Jun;6(2):206-210. doi: 10.1177/2397198320975872. Epub 2020 Nov 25.

DOI:10.1177/2397198320975872
PMID:35386743
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8892937/
Abstract

Parry Romberg disease and En Coupe de Sabre Scleroderma are frequently associated disorders that affect the face and can cause severe aesthetic and functional impairment. Systemic immunosuppression is the gold standard of first-line treatment in the pediatric rheumatology standpoint although it is often delayed in the pediatric dermatology clinics and more often used in cases of refractory neurological impairment. We report on a case with dental root resorption and severe periodontal bone inflammation detected on magnetic resonance imaging, which was successfully treated with the anti-IL-6 agent tocilizumab.

摘要

帕里-龙贝格病和剑状硬皮病是常伴发的疾病，会累及面部，可导致严重的美观和功能损害。从儿科风湿病学角度来看，全身免疫抑制是一线治疗的金标准，尽管在儿科皮肤科诊所这种治疗常常延迟，且更多用于难治性神经功能损害的病例。我们报告了一例磁共振成像检测到牙根吸收和严重牙周骨炎症的病例，该病例用抗白细胞介素-6药物托珠单抗成功治疗。