Abbou Widad, Guerrouj Imane, Tiabi Mahdi, Derouich Yassine, Bennani Amal, Benhaddou Houssain, Skiker Imane, Kamaoui Imane
Department of Radiology, Mohammed VI University hospital, faculty of Medicine, University Mohammed first, Oujda, Morocco.
Department of anatomopathology, Mohammed VI University hospital, faculty of Medicine, University Mohammed first, Oujda, Morocco.
Radiol Case Rep. 2022 Apr 4;17(6):1866-1869. doi: 10.1016/j.radcr.2022.02.060. eCollection 2022 Jun.
Ganglioneuromas are benign tumors of the sympathetic nervous system, rarely found in the presacral region. In this study, we report the case of presacral ganglioneuroma in an 8-year-old girl, who complained of abdominal pain with diarrhea and abdominal distension. Ultrasound showed a large hypoechoic pelvic mass complicated by right ureter hydronephrosis. the CT and MRI confirm the presence of a presacral tissue mass with heterogeneous enhancement after contrast injection. The child underwent a complete surgical resection, and the anatomopathological study returned in favor of a ganglioneuroma. The presacral ganglioneuroma is an extremely rare tumor in that only twenty cases have been reported in the literature. 3 of which were less than 8-years-old. Through our case, we will review the epidemiological, clinical, radiological and therapeutic characteristics of this type of tumor.
神经节神经瘤是交感神经系统的良性肿瘤，很少见于骶前区域。在本研究中，我们报告了一名8岁女孩骶前神经节神经瘤的病例，该女孩主诉腹痛伴腹泻和腹胀。超声显示盆腔有一个大的低回声肿块，并伴有右侧输尿管积水。CT和MRI证实骶前有一个组织肿块，注射造影剂后呈不均匀强化。该患儿接受了完整的手术切除，解剖病理学研究结果支持神经节神经瘤的诊断。骶前神经节神经瘤是一种极其罕见的肿瘤，文献中仅报道过20例，其中3例患者年龄小于8岁。通过我们的病例，我们将回顾这类肿瘤的流行病学、临床、放射学和治疗特征。
