Cicenia Marianna, Drago Fabrizio
Pediatric Cardiology and Arrhythmia/Syncope Complex Unit, Bambino Gesù Children's Hospital, IRCCS, 00146 Rome, Italy.
J Cardiovasc Dev Dis. 2022 Mar 27;9(4):98. doi: 10.3390/jcdd9040098.
Arrhythmogenic cardiomyopathy (ACM) is a cardiomyopathy characterized by the occurrence of a high risk of life-threatening ventricular arrhythmias and sudden cardiac death even at presentation. Diagnosis, evolution and outcomes in adults have been extensively reported, but little data in pediatric population are available. Risk stratification in this particular setting is still a matter of debate and new risk factors are needed in a model of an ever more "individualized medicine".
致心律失常性心肌病（ACM）是一种心肌病，其特征是即使在发病时也存在发生危及生命的室性心律失常和心源性猝死的高风险。关于成人ACM的诊断、病情演变及预后已有大量报道，但儿科人群的数据却很少。在这种特殊情况下的风险分层仍是一个有争议的问题，在日益“个体化医疗”的模式下，还需要新的风险因素。
