Borni Mehdi, Jarraya Firas, Cherif Ines, Zghal Mouna, Gouiaa Naouraz, Boudawara Mohamed Zaher
Department of Neurosurgery, UHC Habib Bourguiba, Street Majida Boulila, Sfax 3029, Tunisia.
Department of Neurosurgery, Valenciennes Hospital Center, Valenciennes, France.
Radiol Case Rep. 2022 Apr 18;17(6):2186-2190. doi: 10.1016/j.radcr.2022.03.094. eCollection 2022 Jun.
Thalamic astrocytomas are rare central nervous system tumors that account for 1%-1.5% of all brain tumors. Their Clinical features depend on anatomical involvement. For these tumors, gross total resection is so difficult due to their deep location and also the infiltration of the optic pathway or brain stem. Unilateral adult thalamic locations are rarely described in the literature. Their radiological features often suggest lymphoma. The authors report here a new case of a primary unilateral thalamic pilocytic astrocytoma mimicking lymphoma diagnosed after a stereotactic core biopsy in a 62-year-old male patient with von Recklinghausen's disease and which is responsible for Dejerine-Roussy syndrome. The authors will proceed with a comprehensive review of literature regarding this rare entity.
丘脑星形细胞瘤是罕见的中枢神经系统肿瘤,占所有脑肿瘤的1%-1.5%。其临床特征取决于解剖结构受累情况。对于这些肿瘤,由于其位置较深且侵犯视路或脑干,很难进行全切。单侧成人丘脑部位的情况在文献中鲜有描述。其影像学特征常提示淋巴瘤。本文作者报告了一例新的原发性单侧丘脑毛细胞型星形细胞瘤病例,该病例在一名患有冯·雷克林豪森病的62岁男性患者中经立体定向穿刺活检后被诊断为疑似淋巴瘤,且该肿瘤导致了丘脑综合征。作者将对有关这一罕见疾病的文献进行全面综述。