男性小儿患者并发多囊性发育不良肾、后尿道瓣膜和输尿管口囊肿：病例报告。

Concurrent Multicystic Dysplastic Kidney, Posterior Urethral Valves, and Obstructive Ureterocele in a Male Pediatric Patient: A Case Report.

机构信息

Division of Pediatric Urology, Department of Surgery, IWK Health Centre, Halifax, Nova Scotia, Canada; Department of Urology, Dalhousie University, Halifax, Nova Scotia, Canada.

出版信息

Urology. 2022 Jul;165:e17-e19. doi: 10.1016/j.urology.2022.04.019. Epub 2022 Apr 30.

DOI:10.1016/j.urology.2022.04.019

PMID:35504454

Abstract

Congenital anomalies of the kidney and urinary tract (CAKUT) are diagnosed in approximately 3-6 per 1000 live births and represent a spectrum of urologic conditions impacting the kidneys, ureter, bladder, and urethra. Although both are considered under the classification of CAKUT, there is no known unifying pathophysiologic mechanism for ureteroceles and posterior urethral valves with only 1 case report noted in the literature. Herein we report the only documented case of a patient with CAKUT related to posterior urethral valves, ureterocele, and multicystic dysplastic kidney.

摘要

先天性肾和尿路异常（CAKUT）在大约每 1000 例活产中诊断出 3-6 例，代表了影响肾脏、输尿管、膀胱和尿道的一系列泌尿科疾病。尽管两者都被认为属于 CAKUT 类别，但输尿管囊肿和后尿道瓣膜的病理生理机制没有已知的统一机制，文献中仅报道了 1 例。在此，我们报告了唯一一例与后尿道瓣膜、输尿管囊肿和多囊性发育不良肾相关的 CAKUT 患者病例。