Servicio de Oftalmología, Hospital Universitario Central de Asturias, Oviedo, Asturias, Spain.
Servicio de Oftalmología, Hospital Universitario Central de Asturias, Oviedo, Asturias, Spain.
Arch Soc Esp Oftalmol (Engl Ed). 2022 May;97(5):290-294. doi: 10.1016/j.oftale.2021.02.009. Epub 2021 Dec 27.
A 38-year-old man who attended the emergency department with headache, accompanied by vomiting, bradypsychia and gait instability, for which he was admitted to Neurology for study. During his admission, he began to present bilateral hearing loss and blurred vision in the left eye, with areas of arterial occlusion and hyperfluorescence of the arterial wall being observed in the ophthalmological examination. As a result, he was diagnosed with Susac syndrome. He was treated with systemic corticosteroids, as well as with rituximab and subsequently, with intravenous immunoglobulins and mycophenolate mofetil. The patient managed to preserve visual acuity, with gait instability and bilateral hearing loss as sequelae. Early diagnosis of Susac syndrome is important, because a delay in the start of treatment can lead to irreversible sequelae such as deafness, blindness or neurological involvement.
一位 38 岁男性，因头痛、呕吐、精神运动迟缓伴步态不稳就诊于急诊科，随后被收入神经内科进行研究。住院期间，他开始出现双侧听力损失和左眼视力模糊，眼科检查发现动脉闭塞和动脉壁荧光增强。因此，他被诊断为 Susac 综合征。他接受了全身皮质类固醇治疗，以及利妥昔单抗治疗，随后还接受了静脉注射免疫球蛋白和霉酚酸酯治疗。患者设法保留了视力，留有步态不稳和双侧听力损失等后遗症。早期诊断 Susac 综合征很重要，因为治疗开始的延迟可能导致不可逆转的后遗症，如耳聋、失明或神经受累。
