Bergamini María L, Martínez Riccetti María C, Kiang Juan A, Urquizo Mauricio, Noriega Susana
Recuperación Cardiovascular Infantil, Servicio de Cirugía Cardiovascular Infantil, Hospital Nacional Posadas, El Palomar, Argentina.
Servicio de Cirugía Cardiovascular Infantil, Departamento Quirúrgico, Hospital Nacional Posadas, El Palomar, Argentina.
Arch Argent Pediatr. 2022 Jun;120(3):e133-e136. doi: 10.5546/aap.2022.e133.
The ring-sling complex is an association between pulmonary artery sling and congenital tracheal stenosis. Pulmonary artery sling is a rare form of vascular ring in congenital heart disease. The clinical case of a child with inspiratory laryngeal stridor associated with respiratory distress is presented, evaluated in another center where respiratory endoscopy was performed, observing extrinsic tracheal compression. Given the clinical suspicion of a vascular ring, CT angiography was requested, confirming the diagnosis of pulmonary artery sling. He was referred to our hospital and during the surgical intervention a new respiratory endoscopy and tracheobronchography were performed, reaching the diagnosis of congenital tracheal stenosis, right accessory bronchus (pig bronchus) and complete vascular rings, both repaired in the same surgical act.
环状吊带复合体是一种肺动脉吊带与先天性气管狭窄的关联。肺动脉吊带是先天性心脏病中一种罕见的血管环形式。本文介绍了一名患有吸气性喉喘鸣并伴有呼吸窘迫的儿童的临床病例,该病例在另一个进行了呼吸内镜检查的中心进行评估,观察到气管外部受压。鉴于临床怀疑有血管环,遂进行了CT血管造影,确诊为肺动脉吊带。该患儿被转诊至我院,在手术干预过程中,再次进行了呼吸内镜检查和气管支气管造影,诊断为先天性气管狭窄、右副支气管(猪支气管)和完全性血管环,均在同一次手术中修复。