肾上腺中的一种二合一肿瘤：具有髓脂肪瘤样分化的功能性肾上腺皮质腺瘤。
A Two-in-One Tumor in the Adrenal: A Functional Adrenocortical Adenoma with Myelolipomatous Differentiation.
作者信息
Bhardwaj Sunny, Deshpande Rohit Sanjay, Kumar Santosh, Mitra Suvradeep
机构信息
Department of Histopathology, PGIMER, Chandigarh, India.
Department of Urology, PGIMER, Chandigarh, India.
出版信息
Fetal Pediatr Pathol. 2023 Feb;42(1):161-166. doi: 10.1080/15513815.2022.2072423. Epub 2022 May 10.
BACKGROUND
Adrenocortical adenoma (ADA) and myelolipoma are two common benign neoplasms of the adrenal cortex that have been reported to occur together.
CASE REPORT
A 14-year-old girl presented with the features of ACTH-independent endogenous Cushing syndrome. Abdominal CECT revealed a left adrenal 2.3 × 1.8 × 1.5 cm arterially enhancing nodular lesion with central hypodensity. Histologically, this was an ADA with oncocytic change and myelolipomatous differentiation/metaplasia.
DISCUSSION/CONCLUSION: ADA with myelolipomatous differentiation/metaplasia can occur in the pediatric age group.
背景
肾上腺皮质腺瘤（ADA）和肾上腺髓质脂肪瘤是肾上腺皮质的两种常见良性肿瘤，据报道可同时发生。
病例报告
一名14岁女孩表现为促肾上腺皮质激素非依赖性内源性库欣综合征的特征。腹部增强CT显示左肾上腺有一个2.3×1.8×1.5cm的结节状病变，动脉期强化，中央低密度。组织学检查显示，这是一个具有嗜酸性细胞改变和髓质脂肪瘤分化/化生的ADA。
讨论/结论：具有髓质脂肪瘤分化/化生的ADA可发生于儿童年龄组。
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