Oncology (Williston Park). 2022 May 9;36(5):293-305. doi: 10.46883/2022.25920960.
The peripheral T-cell lymphomas (PTCLs) are a notoriously diverse family of non-Hodgkin lymphomas with generally aggressive biology. Clinical management is challenging given a largely inadequate literature base comprised of few randomized trials and heterogeneous observational reports. Herein, we provide an account of our practice in the treatment of the 3 most common nodal PTCLs: PTCL, not otherwise specified, angioimmunoblastic T-cell lymphoma, and anaplastic large cell lymphoma (ALCL). In the up-front setting, we employ anthracycline-based induction, with the incorporation of brentuximab vedotin for all those with ALCL and consideration in those with other CD30-expressing PTCLs based on improved progression-free and overall survival in the absence of additional toxicity in the ECHELON-2 trial. We strongly consider high-dose therapy with autologous stem cell rescue in first complete remission. In the relapsed or refractory (R/R) setting, we often look to clinical trials or choose from 4 FDA-approved single agents-belinostat, brentuximab vedotin, romidepsin, and pralatrexate-based on tumor phenotype and side-effect profiles. Our goal in the R/R setting is achievement of complete remission followed by allogeneic transplant with curative intent in appropriate candidates or long-term disease control in others. Numerous investigational agents are advancing through trials and have potential to alter standards of care in the near future.
外周 T 细胞淋巴瘤(PTCLs)是一组众所周知的异质性非霍奇金淋巴瘤,其生物学行为通常具有侵袭性。由于文献基础主要由少数随机试验和异质性观察报告组成,因此临床管理具有挑战性。在此,我们介绍了我们在治疗 3 种最常见的结外 PTCLs(PTCL-NOS、血管免疫母细胞性 T 细胞淋巴瘤和间变大细胞淋巴瘤)方面的治疗实践。在初始治疗中,我们采用蒽环类药物为基础的诱导治疗,并在所有 ALCL 患者中加入 Brentuximab Vedotin,而在其他 CD30 表达的 PTCL 患者中,根据 ECHELON-2 试验中无额外毒性的情况下,无进展生存期和总生存期得到改善,考虑使用该药。我们强烈考虑在首次完全缓解时进行高剂量治疗和自体干细胞挽救。在复发或难治性(R/R)患者中,我们通常会根据肿瘤表型和副作用特征,在临床试验或 4 种美国食品药品监督管理局批准的单药中进行选择,包括贝林司他、Brentuximab Vedotin、罗米地辛和普拉曲沙。我们在 R/R 患者中的目标是达到完全缓解,然后在合适的患者中进行异基因移植以达到治愈目的,或在其他患者中进行长期疾病控制。许多研究药物正在通过临床试验进行,在不久的将来可能会改变治疗标准。