Evola Giuseppe, Schillaci Riccardo, Reina Martina, Caruso Giovambattista, D'Angelo Maria, Reina Giuseppe Angelo
General and Emergency Surgery Department, Garibaldi Hospital, Catania, Italy.
General Surgery Department, San Salvatore Hospital, Paternò (Catania), Italy.
Int J Surg Case Rep. 2022 Jun;95:107152. doi: 10.1016/j.ijscr.2022.107152. Epub 2022 May 3.
Liposarcoma (LPS) represents the most common type of retroperitoneal sarcoma (RPS) and can be classified into four subtypes. Preoperative diagnosis of retroperitoneal liposarcoma (RLPS) is a challenge because of its late and nonspecific clinical presentation. Imaging may be helpful for determining the correct diagnosis. Surgery represents a potentially curative treatment of RLPS.
A 55-year-old Caucasian female presented to the Emergency Department with a two-day history of abdominal pain, abdominal distension, inability to pass gas or stool, nausea, vomiting and lipothymia. Abdominal examination revealed abdominal distention, abdominal pain without obvious muscle guarding and a giant non-tender mass. Laboratory tests reported neutrophilic leukocytosis and anemia. Abdominal contrast-enhanced computed tomography (CECT) showed a heterogeneous and hypodense giant retroperitoneal mass compressing and displacing the surrounding organs and vessels. The patient underwent excision of a giant retroperitoneal mass. The postoperative course of the patient was uneventful.
RLPS is a malignant neoplasm that can slowly grow to enormous size with possible involvement of adjacent organs and vessels; it may recur locally and has a minimal capacity to metastasize. Preoperative diagnosis and staging of RLPS are important to establish appropriate management and prognosis. Surgery represents the gold standard for non-metastatic RLPS treatment.
RLPS is a rare malignant neoplasm generally difficult to detect early due to its late and nonspecific clinical presentation. CECT represents the most commonly used modality for diagnosis, staging and preoperative evaluation. Surgery represents the appropriate treatment of non-metastatic RLPS.
脂肪肉瘤（LPS）是腹膜后肉瘤（RPS）最常见的类型，可分为四种亚型。腹膜后脂肪肉瘤（RLPS）的术前诊断具有挑战性，因为其临床表现出现较晚且不具有特异性。影像学检查可能有助于做出正确诊断。手术是RLPS潜在的治愈性治疗方法。
一名55岁的白种女性因腹痛、腹胀、无法排气或排便、恶心、呕吐及晕厥两天就诊于急诊科。腹部检查发现腹胀、腹痛但无明显肌紧张，以及一个巨大的无压痛肿块。实验室检查报告显示中性粒细胞增多和贫血。腹部增强计算机断层扫描（CECT）显示一个不均匀的低密度巨大腹膜后肿块，压迫并推移周围器官和血管。患者接受了巨大腹膜后肿块切除术。术后恢复过程顺利。
RLPS是一种恶性肿瘤，可缓慢生长至巨大体积，可能累及相邻器官和血管；它可能局部复发，转移能力极小。RLPS的术前诊断和分期对于制定合适的治疗方案和判断预后很重要。手术是未发生转移的RLPS治疗的金标准。
RLPS是一种罕见的恶性肿瘤，由于其临床表现出现较晚且不具有特异性，通常难以早期发现。CECT是诊断、分期及术前评估最常用的检查方式。手术是未发生转移的RLPS的合适治疗方法。
