Céspedes López Roberto, Amutio Díez Elena, Martín Martitegui Xabier, Balerdi Malcorra Amaia, Insunza Oleaga Lucia, Arzuaga-Méndez Javier, Moreno Gámiz Maite, Saiz Camín Mónica, Aberasturi Plata Yoseba, García-Ruíz Juan Carlos
Hematology Banc de Sang i Teixits BST-GIRONA Girona Spain.
Hematology Hospital Universitario Cruces Barakaldo Spain.
Clin Case Rep. 2022 May 9;10(5):e05742. doi: 10.1002/ccr3.5742. eCollection 2022 May.
Thymomas are tumours frequently associated with autoimmune manifestations or immunodeficiencies like Good syndrome. In rare cases, pure white cells aplasia (PWCA) has been described in association with thymomas. PWCA is characterized by agranulocytosis of autoimmune background primary refractory to granulocyte colony-stimulating factor (G-CSF). It is necessary the use of immunosuppressor to allow granulocyte recovery. Without treatment, it could be fatal.
胸腺瘤是常与自身免疫表现或免疫缺陷(如古德综合征)相关的肿瘤。在罕见情况下,已描述了纯白细胞再生障碍(PWCA)与胸腺瘤相关。PWCA的特征是自身免疫背景的粒细胞缺乏症,对粒细胞集落刺激因子(G-CSF)原发难治。必须使用免疫抑制剂以使粒细胞恢复。未经治疗,可能会致命。