Hirai Yoshimitsu, Iwamoto Ryuta, Iguchi Hideto, Fusamoto Aya, Yata Yumi, Ohashi Takuya, Nishimura Yoshiharu
Department of Thoracic and Cardiovascular Surgery Wakayama Medical University Wakayama Japan.
Department of Human Pathology Wakayama Medical University Wakayama Japan.
Respirol Case Rep. 2022 May 9;10(6):e0958. doi: 10.1002/rcr2.958. eCollection 2022 Jun.
A 71-year-old man, who was found to have a posterior mediastinal tumour, was referred to our hospital. Contrast-enhanced computed tomography (CT) showed a 15-cm soft tissue shadow in the posterior mediastinum, with many affected areas and a gradually increasing pattern. We also detected oligemic areas with poor contrast-filling. There was no invasion into the adjacent vertebral body and the blood vessels penetrating the interior were intact. Positron emission tomography-CT revealed a high maximum standardized uptake level of 4.53 in the mediastinal masses. We performed thoracoscopic surgery for the biopsy. Histological findings showed lymphoplasmacytic infiltration in the fibrous stroma as well as storiform fibrosis. Immunohistochemical examination revealed abundant infiltration of immunoglobulin G4 (IgG4)-positive plasma cells and 40% IgG4/IgG-positive plasma cells. Postoperative serum examinations showed a high serum IgG4 level (570 mg/dl). Accordingly, we diagnosed the patient with IgG4-related fibrosing mediastinitis, a rare manifestation of IgG4-related disease.
一名71岁男性,因发现后纵隔肿瘤转诊至我院。增强计算机断层扫描(CT)显示后纵隔有一个15厘米的软组织阴影,有多个受累区域且呈逐渐增大的形态。我们还检测到造影剂填充不良的少血供区域。未侵犯相邻椎体,穿入内部的血管完整。正电子发射断层扫描-CT显示纵隔肿块的最大标准化摄取值高达4.53。我们进行了胸腔镜手术活检。组织学检查发现纤维基质中有淋巴浆细胞浸润以及席纹状纤维化。免疫组化检查显示免疫球蛋白G4(IgG4)阳性浆细胞大量浸润,IgG4/IgG阳性浆细胞占40%。术后血清检查显示血清IgG4水平较高(570mg/dl)。因此,我们诊断该患者患有IgG4相关性纤维性纵隔炎,这是IgG4相关疾病的一种罕见表现。