Ronald O. Perelman Department of Dermatology, New York University Grossman School of Medicine, 240 East 38th Street, 11th Floor, New York, NY, 10016, USA.
Department of Dermatology, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
Am J Clin Dermatol. 2022 Jul;23(4):499-514. doi: 10.1007/s40257-022-00693-0. Epub 2022 May 18.
Sarcoidosis is a multisystem disorder of unknown etiology characterized by accumulation of granulomas in affected tissue. Cutaneous manifestations are among the most common extrapulmonary manifestations in sarcoidosis and can lead to disfiguring disease requiring chronic therapy. In many patients, skin disease may be the first recognized manifestation of sarcoidosis, necessitating a thorough evaluation for systemic involvement. Although the precise etiology of sarcoidosis and the pathogenic mechanisms leading to granuloma formation, persistence, or resolution remain unclear, recent research has led to significant advances in our understanding of this disease. This article reviews recent advances in epidemiology, sarcoidosis clinical assessment with a focus on the dermatologist's role, disease pathogenesis, and new therapies in use and under investigation for cutaneous and systemic sarcoidosis.
结节病是一种病因不明的多系统疾病,其特征是受累组织中肉芽肿的积累。皮肤表现是结节病最常见的肺外表现之一,可导致需要慢性治疗的毁容性疾病。在许多患者中,皮肤疾病可能是结节病的第一个被识别的表现,需要进行彻底的评估以确定是否存在全身受累。尽管结节病的确切病因和导致肉芽肿形成、持续或消退的发病机制仍不清楚,但最近的研究使我们对这种疾病的认识有了重大进展。本文综述了结节病的流行病学、临床评估(重点是皮肤科医生的作用)、发病机制以及在皮肤和系统性结节病中使用和正在研究的新疗法的最新进展。