Department of Ophthalmology, The Second Xiangya Hospital of Central South University, Changsha, Hunan, China.
Department of Orthopedics, The Second Xiangya Hospital of Central South University, Changsha, Hunan, China.
Technol Health Care. 2022;30(5):1267-1272. doi: 10.3233/THC-213658.
Congenital pseudarthrosis of the clavicle (CPC) is a rare congenital entity with unresolved aetiology and pathogenesis. Nearly 250 cases have been reported to date. CPC is characterized by a definite defect in the mid-clavicle at birth and is usually diagnosed when the deformity becomes evident in late childhood or adolescence. Surgical management is controversial, especially in asymptomatic children, with various techniques reported in the literature.
We report a case of a 6-year-old boy who was diagnosed with CPC during a medical examination for primary school enrollment. Operative treatment included debridement of pseudoarthrosis, internal fixation with third tube plate, and barrel-shaped mono-cortical iliac crest autograft.
A complete bone union was obtained 9 months after the operation, and satisfactory function and cosmetic appearance were observed 4 years and 3 months postoperatively.
In our opinion, reconstruction with barrel-shaped mono-cortical iliac crest autograft was an effective and reproducible surgical technique to treat CPC.
先天性锁骨假关节（CPC）是一种罕见的先天性疾病，其病因和发病机制尚未明确。迄今为止，已有近 250 例病例报告。CPC 的特征是出生时锁骨中段有明确的缺损，通常在儿童后期或青春期出现畸形时才被诊断出来。手术治疗存在争议，特别是对于无症状的儿童，文献中报道了各种技术。
我们报告了一例 6 岁男孩，在小学入学体检时被诊断为 CPC。手术治疗包括假关节清创、第三管板内固定和桶形单皮质髂嵴自体移植。
术后 9 个月获得完全骨愈合，术后 4 年 3 个月观察到满意的功能和美容外观。
我们认为，采用桶形单皮质髂嵴自体移植重建是治疗 CPC 的一种有效且可重复的手术技术。
