一名年轻成人的罕见肾肉瘤：其与肾透明细胞肉瘤的相似之处。

Unusual renal sarcoma in a young adult: its similarities to clear cell sarcoma of the kidney.

作者信息

Ogawa K, Nakashima Y, Kim Y C, Yamabe H, Mizukami T, Kaneko S, Hamashima Y

出版信息

J Urol. 1987 Apr;137(4):730-1. doi: 10.1016/s0022-5347(17)44192-9.

Abstract

We report an unusual case of renal sarcoma in a young adult. Histological examination demonstrated many similarities to the histopathological features of clear cell sarcoma of the kidney. Immunohistochemically, none of the intrinsic tumor cells showed positive staining with the antibodies against the intermediate filament proteins, epithelial membrane antigen, S100 protein, neuron-specific enolase, Leu-7 or myoglobin. The clinical course of this tumor was that of high grade malignancy, resulting in death with generalized metastases 13 months after tumor resection.

摘要

我们报告了一例年轻成人肾肉瘤的罕见病例。组织学检查显示其与肾透明细胞肉瘤的组织病理学特征有许多相似之处。免疫组化结果显示，肿瘤内源性细胞均未对针对中间丝蛋白、上皮膜抗原、S100蛋白、神经元特异性烯醇化酶、Leu-7或肌红蛋白的抗体呈阳性染色。该肿瘤的临床病程为高度恶性，在肿瘤切除后13个月因全身转移而死亡。