Xue Amy S, Buchanan Edward P, Hollier Larry H
From Texas Children's Hospital and Baylor College of Medicine.
Plast Reconstr Surg. 2022 Jun 1;149(6):1209e-1223e. doi: 10.1097/PRS.0000000000009046. Epub 2022 May 25.
After studying this article, the participant should be able to: 1. Understand the craniofacial dysmorphology of craniosynostosis, and the variation of each type. 2. Identify the functional concerns and learn the rationale behind timing of operative intervention. 3. Approach each dysmorphology critically and identify the operative intervention needed to improve form and function 4. Understand and address the specific issues related to syndromic craniosynostosis and be able to delineate management plan.
Craniosynostosis is a condition in which premature fusion of one or more cranial sutures lead to abnormal head shape and growth restriction of the brain. Nonsyndromic craniosynostosis occurs in isolation, and usually involves a single suture, whereas syndromic craniosynostosis may involve multiple sutures and is associated with extracraniofacial findings. Although surgical management can be similar, the treatment plan must take into consideration issues specific to the syndromes. This article aims to provide a concise overview of the authors' current understanding regarding the presentation, treatment principle, surgical option, and debates in craniosynostosis.
在学习本文后,参与者应能够:1. 理解颅缝早闭的颅面畸形以及每种类型的变异。2. 识别功能问题并了解手术干预时机背后的原理。3. 批判性地处理每种畸形并确定改善外形和功能所需的手术干预。4. 理解并解决与综合征性颅缝早闭相关的具体问题,并能够制定管理计划。
颅缝早闭是一种一个或多个颅骨缝线过早融合导致头部形状异常和脑生长受限的病症。非综合征性颅缝早闭单独发生,通常累及单一缝线,而综合征性颅缝早闭可能累及多个缝线并伴有颅外面部表现。尽管手术管理可能相似,但治疗计划必须考虑综合征特有的问题。本文旨在对作者目前关于颅缝早闭的表现、治疗原则、手术选择及相关争议的理解作简要概述。