Mansour Marah, Al-Ghotani Basel, Abo-Shdeed Bana, Jannoud Omaya
Faculty of Medicine, Tartous University, Tartous, Syrian Arab Republic.
Faculty of Medicine of Damascus University, Damascus, Syrian Arab Republic.
Ann Med Surg (Lond). 2022 May 4;77:103725. doi: 10.1016/j.amsu.2022.103725. eCollection 2022 May.
Idiopathic retinal vasculitis, aneurysms, and neuroretinitis (IRVAN) syndrome is a rare retinal defect. It has a female predominance. The staging of IRVAN was defined depending on ocular criteria.
A 30-year-old female patient presented with floaters in the left eye. One year later, it was diagnosed with Fluorescein fundus angiography (FFA) at stage Ⅲ of IRVAN syndrome. After one year, the right eye was affected, diagnosed at stage Ⅱ, and successfully treated with heavy Pan-Retinal Photocoagulation (PRP).
IRVAN Syndrome is an extremely rare retinal defect which has female predominance. The etiology of this syndrome still idiopathic. The most encountered symptoms are blurred vision and vision loss. FFA is the best diagnostic investigation to reveal the retinal abnormalities. Many suggested protocols were mentioned to treat IRVAN Syndrome. Our experience suggests IRVAN Syndrome a differential diagnosis for patients with floaters, and assures that PRP is an affective curement for late stages of IRVAN Syndrome.
Heavy PRP was used successfully for stage II and III. The case emphasizes the importance of early diagnosis to assert the complications. Furthermore, IRVAN syndrome should be considered as a differential diagnosis in patients with floaters. Therefore, heavy PRP is highly recommended as a suitable treatment for IRVAN syndrome.
特发性视网膜血管炎、动脉瘤和神经视网膜炎(IRVAN)综合征是一种罕见的视网膜疾病。女性患者更为多见。IRVAN综合征的分期是根据眼部标准来定义的。
一名30岁女性患者左眼出现飞蚊症。一年后,通过荧光素眼底血管造影(FFA)诊断为IRVAN综合征Ⅲ期。一年后,右眼也受到影响,诊断为Ⅱ期,并通过全视网膜光凝术(PRP)成功治疗。
IRVAN综合征是一种极为罕见的视网膜疾病,女性更为多见。该综合征的病因仍不明。最常见的症状是视力模糊和视力丧失。FFA是揭示视网膜异常的最佳诊断检查。文中提到了许多治疗IRVAN综合征的建议方案。我们的经验表明,IRVAN综合征应作为飞蚊症患者的鉴别诊断,并且确保PRP是IRVAN综合征晚期的有效治疗方法。
全视网膜光凝术(PRP)成功用于Ⅱ期和Ⅲ期患者。该病例强调了早期诊断以预防并发症的重要性。此外,IRVAN综合征应被视为飞蚊症患者的鉴别诊断。因此,强烈推荐全视网膜光凝术(PRP)作为IRVAN综合征的合适治疗方法。