Jo Jeong Jun, Kim Yun Seok, Kim Gun-Jik, Kim Jae Hyun
Department of Thoracic and Cardiovascular Surgery, Keimyung University Dongsan Hospital, Keimyung University School of Medicine, Daegu, Korea.
Department of Thoracic and Cardiovascular Surgery, Kyungpook National University Hospital, School of Medicine, Kyungpook National University, Daegu, Korea.
J Chest Surg. 2022 Jun 5;55(3):243-245. doi: 10.5090/jcs.22.008.
True aneurysms of the coronary artery after aortic root replacement in Marfan syndrome patients are very rare. An anomalous origin of the right coronary artery (RCA) from the left sinus of Valsalva adds complexity during aortic root surgery. We present a case of a 37-year-old male patient with Marfan syndrome who had an RCA anomaly and a 4.5-cm true aneurysm of the common coronary button 14 years after a previous Bentall procedure. A redo Bentall operation and hemi-arch replacement were successfully performed. The anomalous origin of the RCA from the left sinus of Valsalva was safely divided and anastomosed as separate coronary buttons to the prosthetic composite valve graft. To prevent coronary button aneurysms after aortic root surgery in Marfan patients, the coronary buttons and the corresponding side holes on the prosthetic graft must be reduced to the maximum possible extent.
马凡综合征患者在主动脉根部置换术后发生冠状动脉真性动脉瘤极为罕见。右冠状动脉(RCA)起源于左冠窦的异常情况会增加主动脉根部手术的复杂性。我们报告一例37岁男性马凡综合征患者,其在先前的Bentall手术14年后出现RCA异常及4.5厘米的冠状动脉总钮扣真性动脉瘤。成功实施了再次Bentall手术及半弓置换术。起源于左冠窦的异常RCA被安全离断,并作为独立的冠状动脉钮扣吻合至人工复合瓣膜移植物。为防止马凡综合征患者主动脉根部手术后发生冠状动脉钮扣动脉瘤,必须尽可能最大程度减小冠状动脉钮扣及人工移植物上相应侧孔的尺寸。