Sh Milad Etemadi, Tajmiri Golnaz
Department of Oral and Maxillofacial Surgery, Dental Implants Research Center, Dental Research Institute, School of Dentistry, Isfahan University of Medical Sciences, Isfahan, Iran.
Dental Implants Research Center, Dental Research Institute, Isfahan University of Medical Sciences, Isfahan, Iran.
Dent Res J (Isfahan). 2022 Apr 27;19:38. eCollection 2022.
Crouzon syndrome is an autosomal dominant trait, leading to midface deficiency, undeveloped orbits, short nasal dorsum, and exophthalmos as the typical clinical features. Early correction of craniofacial problems can improve patients' quality of life, but many of these patients with Crouzon syndrome are seeking treatment in older ages when they are missed for multidisciplinary management and distraction technique in proper timing. Modified LeFort III osteotomy is one of the treatment options that can be used for proper resolution in adult patients. The present case report study aims to describe a patient with midface deficiency due to the Crouzon syndrome who has undergone a combination of modified LeFort III osteotomy with the periocular approach and LeFort I osteotomy, nasal dorsum augmentation accompanied by genioplasty, wholly as a single surgical procedure which has been shown that can result in highly satisfactory outcomes for both patient and surgeon.
克鲁宗综合征是一种常染色体显性性状，典型临床特征为面中部发育不全、眼眶发育不良、鼻背短小和眼球突出。早期矫正颅面问题可改善患者生活质量，但许多克鲁宗综合征患者就诊时年龄较大，错过了多学科管理和适时的牵引技术治疗时机。改良勒福III型截骨术是可用于成年患者恰当矫治的治疗选择之一。本病例报告研究旨在描述一名因克鲁宗综合征导致面中部发育不全的患者，该患者接受了改良勒福III型截骨术联合眼周入路及勒福I型截骨术、鼻背增高术并同期行颏成形术，作为单一手术操作，结果显示对患者和外科医生而言均能取得非常满意的效果。
