Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital, Columbus, OH, USA.
Division of Pediatric General and Thoracic Surgery, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.
Semin Pediatr Surg. 2022 Apr;31(2):151165. doi: 10.1016/j.sempedsurg.2022.151165. Epub 2022 Apr 20.
Total Colonic Hirschsprung Disease (HD) can be challenging from a diagnostic and management standpoint and occurs in around 8% of cases of HD. Long term outcomes are difficult to compare due to variation in length of aganglionosis, chosen surgical techniques, and terminology utilized in the literature. In this review we highlight some of the management controversies and clinical challenges and emphasize future areas of suggested collaboration and research.
全结肠型先天性巨结肠（HD）在诊断和治疗方面具有挑战性，约占 HD 病例的 8%。由于无神经节细胞的长度、选择的手术技术以及文献中使用的术语存在差异，长期预后难以比较。在这篇综述中，我们强调了一些治疗争议和临床挑战，并强调了未来建议合作和研究的领域。
