Neonatology Unit, Department of Pediatrics, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal.
Department of Pediatric and Neonatal Surgery, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal.
JNMA J Nepal Med Assoc. 2022 Jun 1;60(250):565-568. doi: 10.31729/jnma.7462.
Congenital diaphragmatic hernia is an anatomical defect of the diaphragm that is often associated with serious cardiopulmonary complications. It can also be associated with many other problems like multi systemic anomalies, chromosomal aneuploidy and prematurity. Of these, cardiac defects, liver herniation and prematurity seem to have a pivotal role in affecting the outcomes of repair. We hereby present a preterm newborn with such multiple defects repaired on 15th day of life and post operatively managed in a Neonatal Intensive Care Unit with a successful outcome. The key learning objective for our team in this case was to identify the steps taken that led to a successful management of a low birth weight preemie with multiple defects in a resource limited set up.
congenital diaphragmatic hernia; preterm; surgical repair; ventricular septal defect.
先天性膈疝是一种膈肌的解剖缺陷,常伴有严重的心肺并发症。它也可能与许多其他问题有关,如多系统异常、染色体非整倍体和早产。其中,心脏缺陷、肝脏疝出和早产似乎在影响修复结果方面起着关键作用。在此,我们介绍了一例患有多种缺陷的早产儿,在生命的第 15 天接受了手术修复,并在新生儿重症监护病房接受了成功的术后管理。我们团队在这个病例中的关键学习目标是确定在资源有限的情况下,成功管理患有多种缺陷的低体重早产儿所采取的步骤。
先天性膈疝;早产儿;手术修复;室间隔缺损。