Staged repair of supravalvular aortic stenosis associated with severe multiple peripheral pulmonary stenoses: report of extended peripheral pulmonary arterioplasty.

This paper describes surgical experience in supravalvular aortic stenosis associated with severe multiple peripheral pulmonary stenoses treated by a staged approach: initial staged repair of the bilateral pulmonary stenoses by arterioplasty through a thoracotomy and later definitive intracardiac repair of supra-valvular aortic stenosis. Our experience in two cases proved that the peripheral pulmonary arteries could be exposed up to the segmental branches by dissection from the pulmonary hilum through a lateral thoracotomy without damaging the lung parenchyma. The stenotic areas could then be repaired with either a bifurcated or trifurcated pericardial patch.