College of Medicine and Life Sciences, University of Toledo, Toledo, Ohio, USA.
Department of Dermatology, Henry Ford Health System, Detroit, Michigan, USA.
Pediatr Dermatol. 2022 Nov;39(6):992-994. doi: 10.1111/pde.15060. Epub 2022 Jun 23.
Microcystic lymphatic malformation (MiLM), also known as lymphangioma circumscriptum, is a superficial collection of lymphatic vessels measuring <1 cm in the largest diameter, often with a more extensive deeper malformation. It commonly presents as discrete or grouped plaques of clear or hemorrhagic vesicles classically described as "frogspawn"; however, here we describe a case of its unique presentation as firm papules on the lips of a healthy six-year-old child. These skin-colored papules in the absence of vesicles with lymphatic and/or hemorrhagic fluid may not be clinically indicative of MiLM. This case represents a diagnostic challenge due to the unique morphology of pink, fleshy papules as opposed to the clear or hemorrhagic vesicles typically observed in MiLM.
微囊状淋巴管畸形(MiLM),又称淋巴管瘤局限性,是一种直径 <1 厘米的浅层淋巴管集合,通常伴有更广泛的深层畸形。它常表现为离散或成群的清晰或出血性水疱状斑块,经典地描述为“蛙卵状”;然而,在这里我们描述了一个独特的病例,表现为一个健康的六岁儿童嘴唇上的坚实丘疹。这些无水疱、含有淋巴和/或血性液体的皮肤色丘疹在临床上可能不是 MiLM 的指征。由于粉红色肉质丘疹的独特形态与 MiLM 中通常观察到的清晰或出血性水疱相反,因此该病例构成了诊断挑战。