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嗜铬细胞瘤继发的非典型变异型应激性心肌病。

Atypical variant takotsubo cardiomyopathy secondary to pheochromocytoma.

作者信息

Kokkapuni Nikhil, Thieu Michelle, Bana Sinan Ali, Cherian Reba, Haberman Amy

机构信息

Texas A&M University College of Medicine, Bryan, Texas.

Department of Radiology, Baylor University Medical Center, Dallas, Texas.

出版信息

Proc (Bayl Univ Med Cent). 2022 Mar 22;35(4):526-528. doi: 10.1080/08998280.2022.2049574. eCollection 2022.

Abstract

A 39-year-old woman presented with chest pain and elevated troponin levels. Cardiac catheterization demonstrated no coronary artery disease, with findings consistent with atypical variant takotsubo cardiomyopathy. Further workup showed elevated plasma fractionated metanephrines suggestive of pheochromocytoma. Abdominal imaging showed a right adrenal mass, with surgical excision and histopathological evaluation confirming a pheochromocytoma. Pheochromocytomas are a rare cause of takotsubo-like syndrome with an atypical takotsubo variant rarer still.

摘要

一名39岁女性因胸痛和肌钙蛋白水平升高就诊。心脏导管检查显示无冠状动脉疾病,结果符合非典型变异型应激性心肌病。进一步检查显示血浆去甲肾上腺素水平升高,提示嗜铬细胞瘤。腹部影像学检查显示右侧肾上腺肿块,手术切除及组织病理学评估证实为嗜铬细胞瘤。嗜铬细胞瘤是应激性心肌病样综合征的罕见病因,而非典型应激性心肌病变异型更为罕见。

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Pheochromocytoma-Induced Takotsubo Cardiomyopathy.嗜铬细胞瘤诱发的应激性心肌病
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Primary malignant tumors of the adrenal glands.肾上腺原发性恶性肿瘤。
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