Department of Congenital Heart Surgery, University Hospital Center Zagreb, Zagreb, Croatia.
Department of Pediatric Cardiology, University Hospital Center Zagreb, Zagreb, Croatia.
Tex Heart Inst J. 2022 May 1;49(3). doi: 10.14503/THIJ-20-7393.
Total anomalous pulmonary venous return is a congenital heart malformation characterized by anomalous pulmonary venous inflow to the right atrium. Surgical repair typically occurs during the first month of life, and survival beyond that age in untreated patients is unlikely. We report an extreme case of supracardiac total anomalous pulmonary venous return in an infant who survived 7 months despite atypical anomalous inflow without atrial-level communication and with right-to-left shunting only through a patent ductus arteriosus. We stabilized the patient's left-sided heart function before surgically repairing the anomalous venous return 2 months later. Three years postoperatively, the patient was well.
完全性肺静脉异位引流是一种先天性心脏畸形,其特征是肺静脉异常流入右心房。手术修复通常在出生后的第一个月进行,如果未经治疗,患者在该年龄后存活的可能性不大。我们报告了一例婴儿极重度心上型完全性肺静脉异位引流的病例,尽管存在异常的肺静脉回流,但没有房间隔水平的沟通,且只有动脉导管未闭存在右向左分流,该患儿存活了 7 个月。我们在 2 个月后手术修复异常静脉回流之前稳定了患者的左侧心脏功能。术后 3 年,患者情况良好。