Departamento de Córnea y Cirugía Refractiva, Asociación para Evitar la Ceguera en México, Hospital "Dr. Luis Sánchez Bulnes", Mexico City, Mexico.
Clínica Oftalmológica García de Oteyza, Barcelona, Spain.
Arch Soc Esp Oftalmol (Engl Ed). 2022 Jul;97(7):409-412. doi: 10.1016/j.oftale.2021.04.004. Epub 2022 Feb 16.
Intravascular papillary endothelial hyperplasia (IPEH) is characterized by proliferation of endothelial cells usually occurring within a long-standing vascular malformation or tumor. IPEH usually affects neck, head and lower extremities, and few orbital and eyelid cases have been reported. We present a unique case, a 48-years-old man with a purple, elevated, multilobular conjunctival lesion of three-weeks duration that underwent an excisional biopsy. Pathological features revealed intravascular papillary endothelial hyperplasia (Masson's tumor).
血管内乳头状内皮细胞增生症 (IPEH) 的特征是内皮细胞的增殖,通常发生在长期存在的血管畸形或肿瘤内。IPEH 通常影响颈部、头部和下肢,很少有眼眶和眼睑病例报道。我们报告了一个独特的病例,一名 48 岁男性,其结膜有一个紫色、隆起、多叶状病变,病程为 3 周,接受了切除活检。病理特征显示血管内乳头状内皮细胞增生症 (Masson 肿瘤)。