巨大先天性肺气道畸形伴黏液细胞簇 - 病例报告。

Large congenital pulmonary airway malformation with mucinous cell clusters - a case report.

机构信息

Neonatal Intensive Care Unit, Neonatology Department, Centro Hospitalar Universitário de São João, Porto, Portugal; Faculty of Medicine of the University of Porto, Porto, Portugal.

Faculty of Medicine of the University of Porto, Porto, Portugal; Departmentof Cardiothoracic Surgery, Centro Hospitalar Universitário de São João, Porto, Portugal.

出版信息

Port J Card Thorac Vasc Surg. 2022 Jul 3;29(2):67-69. doi: 10.48729/pjctvs.182.

DOI:10.48729/pjctvs.182

PMID:35780409

Abstract

We report the clinical case of a 38 weeks gestational age neonate, antenatally diagnosed with a left large macrocystic pulmonary malformation conditioning dextrocardia. At birth, he presented with respiratory distress requiring non-invasive ventilation with high-flow nasal cannula (HFNC). A left inferior lobectomy was performed via thoracotomy on day 21 of life. Histological features of the lesion were compatible with congenital pulmonary airway malformation (CPAM) type I with muci- nous cell clusters. No surgical complications were reported and the neonate was discharged six days after surgery. Follow-up two months after surgery was unremarkable.

摘要

我们报告了一例 38 周胎龄的新生儿临床病例，该患儿产前诊断为左侧大型肺囊性腺瘤样畸形伴右位心。出生时，患儿出现呼吸窘迫，需要经鼻高流量吸氧（HFNC）进行无创通气。在出生后第 21 天行胸腔镜下左肺下叶切除术。病变的组织学特征与 I 型先天性肺气道畸形（CPAM）相符，伴有黏液细胞簇。患儿无手术并发症，并在术后 6 天出院。术后 2 个月随访无异常。