Souiki Tarik, Belhaj Anas, Ait Abderrhim Abderrahim, Alami Badreeddine, Tahiri Layla, Chbani Laila, Ibn Majdoub Karim, Toughrai Imane, Mazaz Khalid
Faculty of Medicine and Pharmacy of Fez, Sidi Mohammed Ben Abdellah University, Fez, Morocco.
J Surg Case Rep. 2022 Jun 30;2022(6):rjac272. doi: 10.1093/jscr/rjac272. eCollection 2022 Jun.
Dermatofibrosarcoma protuberans (DFSP) is a rare and slowly growing cutaneous tumor with high risk of local invasion and recurrence. Here, we report a case of a DFSP of the anterior abdominal wall diagnosed in a 45-year-old woman. The clinical examination showed an indurated well-limited oval mass localized in the supra-umbilical level and measuring 5 cm by 3 cm. The histological finding of skin biopsy was consistent with the diagnosis of DFSP. A wide local excision was performed while respecting minimum safety margins of 3 cm. The primary closure was possible after advancing the subcutaneous adjacent tissue. The histological examination of the surgical specimen confirmed the DFSP diagnosis and determined safe microscopic margins. After 4 years of regular follow-up, no locoregional or distant recurrence was observed. We discuss through this case the diagnosis difficulties and the particularities of the abdominal wall localization.
隆突性皮肤纤维肉瘤（DFSP）是一种罕见的、生长缓慢的皮肤肿瘤，具有局部侵袭和复发的高风险。在此，我们报告一例45岁女性腹壁前部DFSP病例。临床检查显示，在脐上水平有一个边界清晰的硬结性椭圆形肿块，大小为5厘米×3厘米。皮肤活检的组织学结果与DFSP诊断一致。在保证至少3厘米安全切缘的情况下进行了广泛局部切除。推进相邻皮下组织后可行一期缝合。手术标本的组织学检查证实了DFSP诊断，并确定了安全的显微镜下切缘。经过4年的定期随访，未观察到局部或远处复发。我们通过该病例讨论了诊断难点及腹壁定位的特殊性。
